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Long QT syndrome and left ventricular non-compaction in a family with KCNH2 mutation: A case report

BACKGROUND: Left ventricular non-compaction (LVNC) is an abnormality of the myocardium, characterized by prominent left ventricular trabeculae and deep inter-trabecular recesses. Long QT syndrome (LQTS) is a cardiac ion channelopathy presenting with a prolonged QT interval on resting electrocardiogr...

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Detalles Bibliográficos
Autores principales:	Caiffa, Thomas, Tessitore, Antimo, Leoni, Loira, Reffo, Elena, Chicco, Daniela, D'Agata Mottolese, Biancamaria, Rubinato, Elisa, Girotto, Giorgia, Lenarduzzi, Stefania, Barbi, Egidio, Bobbo, Marco, Di Salvo, Giovanni
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2022
Materias:	Pediatrics
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9386155/ https://www.ncbi.nlm.nih.gov/pubmed/35989994 http://dx.doi.org/10.3389/fped.2022.970240

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