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Kidney involvement in hereditary transthyretin amyloidosis: a cohort study of 103 patients

BACKGROUND: Hereditary transthyretin amyloidosis (ATTRv) is a disabling and life-threatening disease that primarily affects the nervous system and heart. Its kidney involvement has not been systematically studied, particularly in non-V30M mutations, and is not well known to nephrologists. METHODS: W...

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Detalles Bibliográficos
Autores principales: Solignac, Justine, Delmont, Emilien, Fortanier, Etienne, Attarian, Shahram, Mancini, Julien, Daniel, Laurent, Ion, Ioana, Ricci, Jean-Etienne, Robert, Thomas, Habib, Gilbert, Moranne, Olivier, Jourde-Chiche, Noémie
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9394715/
https://www.ncbi.nlm.nih.gov/pubmed/36003663
http://dx.doi.org/10.1093/ckj/sfac118