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Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()

L-type transposition of the great vessels is a rare congenital heart disease in which both the great arteries and the ventricular chambers are reversed. Because this condition preserves a physiologic circulatory pathway, it can be challenging to diagnose in infants with no concurrent cardiac abnorma...

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Detalles Bibliográficos
Autores principales: Everett, Lindsay, Parikh, Ishan, Taxak, Pritee, Albers, Brittany, Joshi, Jonathan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9396308/
https://www.ncbi.nlm.nih.gov/pubmed/36016986
http://dx.doi.org/10.1016/j.radcr.2022.07.094
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author Everett, Lindsay
Parikh, Ishan
Taxak, Pritee
Albers, Brittany
Joshi, Jonathan
author_facet Everett, Lindsay
Parikh, Ishan
Taxak, Pritee
Albers, Brittany
Joshi, Jonathan
author_sort Everett, Lindsay
collection PubMed
description L-type transposition of the great vessels is a rare congenital heart disease in which both the great arteries and the ventricular chambers are reversed. Because this condition preserves a physiologic circulatory pathway, it can be challenging to diagnose in infants with no concurrent cardiac abnormalities. Early detection is essential, however, because these patients will eventually experience severe complications, as the structural right ventricle is unable to function long-term in the systemic position. We report a rare case of L-type transposition of the great vessels in a 32-year-old male who presented in adulthood with tachycardia and palpitations. The initial echocardiogram was inconclusive. Further imaging (cardiac MRI & transesophageal echocardiogram) revealed the inverted anatomy due to the presence of key morphological features, such as the malposed great vessels along with the moderator band and prominent trabeculae within the right ventricle, which was functioning systemically.
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spelling pubmed-93963082022-08-24 Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart() Everett, Lindsay Parikh, Ishan Taxak, Pritee Albers, Brittany Joshi, Jonathan Radiol Case Rep Case Report L-type transposition of the great vessels is a rare congenital heart disease in which both the great arteries and the ventricular chambers are reversed. Because this condition preserves a physiologic circulatory pathway, it can be challenging to diagnose in infants with no concurrent cardiac abnormalities. Early detection is essential, however, because these patients will eventually experience severe complications, as the structural right ventricle is unable to function long-term in the systemic position. We report a rare case of L-type transposition of the great vessels in a 32-year-old male who presented in adulthood with tachycardia and palpitations. The initial echocardiogram was inconclusive. Further imaging (cardiac MRI & transesophageal echocardiogram) revealed the inverted anatomy due to the presence of key morphological features, such as the malposed great vessels along with the moderator band and prominent trabeculae within the right ventricle, which was functioning systemically. Elsevier 2022-08-13 /pmc/articles/PMC9396308/ /pubmed/36016986 http://dx.doi.org/10.1016/j.radcr.2022.07.094 Text en Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Everett, Lindsay
Parikh, Ishan
Taxak, Pritee
Albers, Brittany
Joshi, Jonathan
Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()
title Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()
title_full Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()
title_fullStr Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()
title_full_unstemmed Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()
title_short Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart()
title_sort cardiac mr imaging reveals l-type transposition of the great vessels and failing right heart()
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9396308/
https://www.ncbi.nlm.nih.gov/pubmed/36016986
http://dx.doi.org/10.1016/j.radcr.2022.07.094
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