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Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad

Melkersson-Rosenthal syndrome (MRS) is an uncommon neuro-mucocutaneous disease, clinically characterized by a triad of recurrent facial palsy, orofacial swelling, and fissured tongue. This report presents the case of a 38-year-old female diagnosed with MRS based on its three clinical features. A cor...

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Detalles Bibliográficos
Autores principales: Aoun, Georges, Skandri, Nadia, Ghattas, Hafiza, Maksoud, Carlo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9420175/
https://www.ncbi.nlm.nih.gov/pubmed/36051736
http://dx.doi.org/10.7759/cureus.27427
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author Aoun, Georges
Skandri, Nadia
Ghattas, Hafiza
Maksoud, Carlo
author_facet Aoun, Georges
Skandri, Nadia
Ghattas, Hafiza
Maksoud, Carlo
author_sort Aoun, Georges
collection PubMed
description Melkersson-Rosenthal syndrome (MRS) is an uncommon neuro-mucocutaneous disease, clinically characterized by a triad of recurrent facial palsy, orofacial swelling, and fissured tongue. This report presents the case of a 38-year-old female diagnosed with MRS based on its three clinical features. A corticosteroid (1 mg/kg/day of oral prednisolone) was prescribed for a week, and then tapered off over two weeks by gradually lowering the dose. Regular annual long-term follow-ups were requested to monitor the disease activity.
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spelling pubmed-94201752022-08-31 Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad Aoun, Georges Skandri, Nadia Ghattas, Hafiza Maksoud, Carlo Cureus Dentistry Melkersson-Rosenthal syndrome (MRS) is an uncommon neuro-mucocutaneous disease, clinically characterized by a triad of recurrent facial palsy, orofacial swelling, and fissured tongue. This report presents the case of a 38-year-old female diagnosed with MRS based on its three clinical features. A corticosteroid (1 mg/kg/day of oral prednisolone) was prescribed for a week, and then tapered off over two weeks by gradually lowering the dose. Regular annual long-term follow-ups were requested to monitor the disease activity. Cureus 2022-07-28 /pmc/articles/PMC9420175/ /pubmed/36051736 http://dx.doi.org/10.7759/cureus.27427 Text en Copyright © 2022, Aoun et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Dentistry
Aoun, Georges
Skandri, Nadia
Ghattas, Hafiza
Maksoud, Carlo
Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad
title Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad
title_full Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad
title_fullStr Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad
title_full_unstemmed Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad
title_short Melkersson-Rosenthal Syndrome in a 38-Year-Old Female Patient: A Rare Case With Complete Triad
title_sort melkersson-rosenthal syndrome in a 38-year-old female patient: a rare case with complete triad
topic Dentistry
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9420175/
https://www.ncbi.nlm.nih.gov/pubmed/36051736
http://dx.doi.org/10.7759/cureus.27427
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