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Deterioration after Liver Transplantation and Transthyretin Stabilizer Administration in a Patient with ATTRv Amyloidosis with a Leu58Arg (p.Leu78Arg) TTR Variant

We herein report a 44-year-old Japanese man with hereditary transthyretin amyloidosis (ATTRv amyloidosis) harboring the variant Leu58Arg (p.Leu78Arg) in TTR in whom we conducted an observational study with liver transplantation (LT) and transthyretin (TTR) stabilizers (tafamidis and diflunisal) for...

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Detalles Bibliográficos
Autores principales:	Hikishima, Sadao, Sakai, Kenji, Akagi, Akio, Yamaguchi, Hiroki, Shibata, Shutaro, Hayashi, Koji, Nakano, Hiroto, Kanemoto, Mizuki, Usui, Yuta, Taniguchi, Yu, Komatsu, Junji, Nakamura-Shindo, Keiko, Nozaki, Ichiro, Hamaguchi, Tsuyoshi, Ono, Kenjiro, Iwasa, Kazuo, Yamada, Masahito
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Japanese Society of Internal Medicine 2022
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9424092/ https://www.ncbi.nlm.nih.gov/pubmed/35283385 http://dx.doi.org/10.2169/internalmedicine.8945-21

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