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Ocular manifestations in Kindler syndrome

We aimed describe the chronic ocular sequelae of Kindler syndrome. All cases of Kindler syndrome with ocular involvement that presented to a tertiary eye care center were included. Three cases of Kindler syndrome with ocular changes were reviewed. Case 1 (10 years, female) had recurrent epithelial b...

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Autores principales: Maharana, Prafulla K, Sahay, Pranita, Mandal, Sohini, Nagpal, Ritu, Sharma, Namrata
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9426131/
https://www.ncbi.nlm.nih.gov/pubmed/35791162
http://dx.doi.org/10.4103/ijo.IJO_791_22
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author Maharana, Prafulla K
Sahay, Pranita
Mandal, Sohini
Nagpal, Ritu
Sharma, Namrata
author_facet Maharana, Prafulla K
Sahay, Pranita
Mandal, Sohini
Nagpal, Ritu
Sharma, Namrata
author_sort Maharana, Prafulla K
collection PubMed
description We aimed describe the chronic ocular sequelae of Kindler syndrome. All cases of Kindler syndrome with ocular involvement that presented to a tertiary eye care center were included. Three cases of Kindler syndrome with ocular changes were reviewed. Case 1 (10 years, female) had recurrent epithelial breakdown with severe dry eye and corneal opacity secondary to keratitis. Case 2 (28 years, male) had symblepharon , ocular surface keratinization , and severe dry eye. Case 3 (16 years , female ) had partial limbal stem cell deficiency with dry eye. All cases were treated with topical lubricants, short course of low-potency steroids and immuno-modulators. Attention must be paid to the eye in addition to the oro-an-genital mucosa to avoid longterm ocular sequelae.
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spelling pubmed-94261312022-08-31 Ocular manifestations in Kindler syndrome Maharana, Prafulla K Sahay, Pranita Mandal, Sohini Nagpal, Ritu Sharma, Namrata Indian J Ophthalmol Case Series We aimed describe the chronic ocular sequelae of Kindler syndrome. All cases of Kindler syndrome with ocular involvement that presented to a tertiary eye care center were included. Three cases of Kindler syndrome with ocular changes were reviewed. Case 1 (10 years, female) had recurrent epithelial breakdown with severe dry eye and corneal opacity secondary to keratitis. Case 2 (28 years, male) had symblepharon , ocular surface keratinization , and severe dry eye. Case 3 (16 years , female ) had partial limbal stem cell deficiency with dry eye. All cases were treated with topical lubricants, short course of low-potency steroids and immuno-modulators. Attention must be paid to the eye in addition to the oro-an-genital mucosa to avoid longterm ocular sequelae. Wolters Kluwer - Medknow 2022-07 2022-06-30 /pmc/articles/PMC9426131/ /pubmed/35791162 http://dx.doi.org/10.4103/ijo.IJO_791_22 Text en Copyright: © 2022 Indian Journal of Ophthalmology https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Series
Maharana, Prafulla K
Sahay, Pranita
Mandal, Sohini
Nagpal, Ritu
Sharma, Namrata
Ocular manifestations in Kindler syndrome
title Ocular manifestations in Kindler syndrome
title_full Ocular manifestations in Kindler syndrome
title_fullStr Ocular manifestations in Kindler syndrome
title_full_unstemmed Ocular manifestations in Kindler syndrome
title_short Ocular manifestations in Kindler syndrome
title_sort ocular manifestations in kindler syndrome
topic Case Series
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9426131/
https://www.ncbi.nlm.nih.gov/pubmed/35791162
http://dx.doi.org/10.4103/ijo.IJO_791_22
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