Pulmonary calcinosis associated with Alport syndrome

We report the case of a 48-year-old woman under dialysis from chronic renal failure (CRF) since the age of 27, due to Alport syndrome. The patient underwent routine chest X-ray on which diffuse micronodules were shown. Chest computed tomography showed partially calcified micronodules with centrilobu...

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Detalles Bibliográficos
Autores principales: Mismetti, Valentine, Perquis, Marie-Pierre, Hamdi, Lina, Froudarakis, Marios E., Vergnon, Jean-Michel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9428909/
https://www.ncbi.nlm.nih.gov/pubmed/36060641
http://dx.doi.org/10.1016/j.rmcr.2022.101727
Descripción
Sumario:We report the case of a 48-year-old woman under dialysis from chronic renal failure (CRF) since the age of 27, due to Alport syndrome. The patient underwent routine chest X-ray on which diffuse micronodules were shown. Chest computed tomography showed partially calcified micronodules with centrilobular distribution respecting the subpleural spaces and predominant in the upper lobar regions. Metastatic pulmonary calcinosis was confirmed by the bone scan with an overall course of 29 years. This is the first reported case of pulmonary calcinosis from CRF due to Alport syndrome.

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