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Anesthesia management in living-donor liver transplantation in a patient with carbamoyl phosphate synthetase deficiency: a case report

BACKGROUND: Carbamoyl phosphate synthetase deficiency (CPS1D) is a urea-cycle disorder (UCD). We report successful perioperative management of pediatric living donor liver transplantation (LDLT) in a CPS1D patient. CASE PRESENTATION: A 10-year-old female patient with CPS1D underwent LDLT. Proper adm...

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Detalles Bibliográficos
Autores principales:	Matsushita, Hiroki, Fujiyoshi, Tetsushiro, Yoshimaru, Koichiro, Matsuura, Toshiharu, Mushimoto, Yuichi, Karashima, Yuji, Yamaura, Ken
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Springer Berlin Heidelberg 2022
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9452607/ https://www.ncbi.nlm.nih.gov/pubmed/36070152 http://dx.doi.org/10.1186/s40981-022-00558-9

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