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Immunofluorescence signal intensity measurements as a semi-quantitative tool to assess sarcoglycan complex expression in muscle biopsy

Sarcoglycanopathies are highly heterogeneous in terms of disease progression, muscular weakness, loss of ambulation and cardiac/respiratory involvement. Their clinical severity usually correlates with the residual protein amount, which makes protein quantification extremely relevant. Sarcoglycanopat...

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Detalles Bibliográficos
Autores principales:	Zanotti, Simona, Magri, Francesca, Poggetti, Francesca, Ripolone, Michela, Velardo, Daniele, Fortunato, Francesco, Ciscato, Patrizia, Moggio, Maurizio, Corti, Stefania, Comi, Giacomo Pietro, Sciacco, Monica
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	PAGEPress Publications, Pavia, Italy 2022
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9471914/ https://www.ncbi.nlm.nih.gov/pubmed/36047345 http://dx.doi.org/10.4081/ejh.2022.3418

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