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Altered SOD1 maturation and post-translational modification in amyotrophic lateral sclerosis spinal cord

Aberrant self-assembly and toxicity of wild-type and mutant superoxide dismutase 1 (SOD1) has been widely examined in silico, in vitro and in transgenic animal models of amyotrophic lateral sclerosis. Detailed examination of the protein in disease-affected tissues from amyotrophic lateral sclerosis...

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Detalles Bibliográficos
Autores principales:	Trist, Benjamin G, Genoud, Sian, Roudeau, Stéphane, Rookyard, Alexander, Abdeen, Amr, Cottam, Veronica, Hare, Dominic J, White, Melanie, Altvater, Jens, Fifita, Jennifer A, Hogan, Alison, Grima, Natalie, Blair, Ian P, Kysenius, Kai, Crouch, Peter J, Carmona, Asuncion, Rufin, Yann, Claverol, Stéphane, Van Malderen, Stijn, Falkenberg, Gerald, Paterson, David J, Smith, Bradley, Troakes, Claire, Vance, Caroline, Shaw, Christopher E, Al-Sarraj, Safa, Cordwell, Stuart, Halliday, Glenda, Ortega, Richard, Double, Kay L
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Oxford University Press 2022
Materias:	Original Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9473357/ https://www.ncbi.nlm.nih.gov/pubmed/35512359 http://dx.doi.org/10.1093/brain/awac165

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