Indolent multicentric chordoma – A previously undescribed entity: A Case report and literature review

BACKGROUND: Chordomas are rare neuraxial tumors arising from remnants of primitive notochord. They are generally slow-growing malignant neoplasms. Only four adult cases of multicentric chordomas have been reported, all with aggressive and rapid growth. Here, we present an unusual case of indolent mu...

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Detalles Bibliográficos
Autores principales: Jenson, Amanda Vilate, Taylor, Daniel G., Ayala, Alberto, Jackson, Robert Evan, Baskin, David S.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Scientific Scholar 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9479634/
https://www.ncbi.nlm.nih.gov/pubmed/36128155
http://dx.doi.org/10.25259/SNI_507_2022
Descripción
Sumario:BACKGROUND: Chordomas are rare neuraxial tumors arising from remnants of primitive notochord. They are generally slow-growing malignant neoplasms. Only four adult cases of multicentric chordomas have been reported, all with aggressive and rapid growth. Here, we present an unusual case of indolent multicentric chordomas involving cervical and thoracic spine, sacrum, and calvarium. CASE DESCRIPTION: A 60-year-old male was found to have multiple lesions throughout his neuroaxis incidentally on workup for colitis. A needle biopsy documented the diagnosis of chordoma. This has been followed for more than 4 years with no progression. CONCLUSION: We present the first reported case of indolent multicentric chordomas. Due to the extreme rarity of indolent multicentric chordomas, close follow-up is needed and recommended.

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