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Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report

BACKGROUND: Aggressive Angiomyxoma is a benign, slowly growing, locally aggressive and recurrent tumour that occurs in the pelvic-perineal region of females in their reproductive years. It presents as a painless, soft, gelatinous mass and metastasizes rarely. Suspicion can be made based on clinical...

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Autores principales: Muskan, Vitasta, Adhikari, Purbesh, Thapa, Baburam Dixit, Shrestha, Ramesh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9484075/
https://www.ncbi.nlm.nih.gov/pubmed/36123742
http://dx.doi.org/10.1186/s12905-022-01847-2
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author Muskan, Vitasta
Adhikari, Purbesh
Thapa, Baburam Dixit
Shrestha, Ramesh
author_facet Muskan, Vitasta
Adhikari, Purbesh
Thapa, Baburam Dixit
Shrestha, Ramesh
author_sort Muskan, Vitasta
collection PubMed
description BACKGROUND: Aggressive Angiomyxoma is a benign, slowly growing, locally aggressive and recurrent tumour that occurs in the pelvic-perineal region of females in their reproductive years. It presents as a painless, soft, gelatinous mass and metastasizes rarely. Suspicion can be made based on clinical examination and radiological imaging but final diagnosis is confirmed only after histopathology and immunohistochemistry. The choice of treatment is surgical wide local excision. CASE PRESENTATION: We hereby present a case of a 19-year, unmarried lady, with a body mass index of 21 kg/m(2), who presented with a chief complaint of painless mass in left vulva which progressively increased in size in the past one year. Clinical examination revealed a large, cauliflower like, exophytic mass of 10 cm × 10 cm size. Radiological imaging confirmed involvement of lymph nodes. Wide local excision with adequate tumour free margin and depth was used as a treatment modality. The diagnosis was confirmed via histopathological examination of the excised specimen. There is no recurrence in the patient up to date. CONCLUSION: Aggressive Angiomyxoma is a rare tumour and it is most often misdiagnosed. This report highlights the importance of considering Aggressive Angiomyxoma as a differential diagnosis of vulval masses and the two-step surgical approach for its treatment in low resource setting.
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spelling pubmed-94840752022-09-20 Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report Muskan, Vitasta Adhikari, Purbesh Thapa, Baburam Dixit Shrestha, Ramesh BMC Womens Health Case Report BACKGROUND: Aggressive Angiomyxoma is a benign, slowly growing, locally aggressive and recurrent tumour that occurs in the pelvic-perineal region of females in their reproductive years. It presents as a painless, soft, gelatinous mass and metastasizes rarely. Suspicion can be made based on clinical examination and radiological imaging but final diagnosis is confirmed only after histopathology and immunohistochemistry. The choice of treatment is surgical wide local excision. CASE PRESENTATION: We hereby present a case of a 19-year, unmarried lady, with a body mass index of 21 kg/m(2), who presented with a chief complaint of painless mass in left vulva which progressively increased in size in the past one year. Clinical examination revealed a large, cauliflower like, exophytic mass of 10 cm × 10 cm size. Radiological imaging confirmed involvement of lymph nodes. Wide local excision with adequate tumour free margin and depth was used as a treatment modality. The diagnosis was confirmed via histopathological examination of the excised specimen. There is no recurrence in the patient up to date. CONCLUSION: Aggressive Angiomyxoma is a rare tumour and it is most often misdiagnosed. This report highlights the importance of considering Aggressive Angiomyxoma as a differential diagnosis of vulval masses and the two-step surgical approach for its treatment in low resource setting. BioMed Central 2022-09-19 /pmc/articles/PMC9484075/ /pubmed/36123742 http://dx.doi.org/10.1186/s12905-022-01847-2 Text en © The Author(s) 2022 https://creativecommons.org/licenses/by/4.0/Open AccessThis article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) . The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/ (https://creativecommons.org/publicdomain/zero/1.0/) ) applies to the data made available in this article, unless otherwise stated in a credit line to the data.
spellingShingle Case Report
Muskan, Vitasta
Adhikari, Purbesh
Thapa, Baburam Dixit
Shrestha, Ramesh
Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report
title Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report
title_full Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report
title_fullStr Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report
title_full_unstemmed Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report
title_short Vulval Aggressive Angiomyxoma in a 19 year teenager: a case report
title_sort vulval aggressive angiomyxoma in a 19 year teenager: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9484075/
https://www.ncbi.nlm.nih.gov/pubmed/36123742
http://dx.doi.org/10.1186/s12905-022-01847-2
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