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Malignant inflammatory myofibroblastic tumor: a rare case presentation

Malignant inflammatory myofibroblastic tumors (IMT) are extremely rare, aggressive tumors with variable presentation. This is a case of a 29-year-old female presented with severe anemia and a large abdominal mass presumed to be a gastrointestinal stromal tumor (GIST). Severe anemia, leukocytosis and...

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Detalles Bibliográficos
Autores principales: Spafford, Megan, Lunn, Danley, Graham, Peter
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9487198/
https://www.ncbi.nlm.nih.gov/pubmed/36148141
http://dx.doi.org/10.1093/jscr/rjac403
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author Spafford, Megan
Lunn, Danley
Graham, Peter
author_facet Spafford, Megan
Lunn, Danley
Graham, Peter
author_sort Spafford, Megan
collection PubMed
description Malignant inflammatory myofibroblastic tumors (IMT) are extremely rare, aggressive tumors with variable presentation. This is a case of a 29-year-old female presented with severe anemia and a large abdominal mass presumed to be a gastrointestinal stromal tumor (GIST). Severe anemia, leukocytosis and thrombocytosis accompanied the presentation. Final pathological assessment yielded a diagnosis of malignant IMT. Given the rarity of these tumors, no established diagnostic criteria exist aside from histological analysis of the tissue, which may result in delays or inappropriate treatment. As these tumors are aggressive in nature, a high index of suspicion is critical to improve outcomes. Further reports on the presentation, diagnosis and treatment of such rare tumors are important to develop clinical diagnostic guidelines to improve diagnosis and treatment and improve outcomes.
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spelling pubmed-94871982022-09-21 Malignant inflammatory myofibroblastic tumor: a rare case presentation Spafford, Megan Lunn, Danley Graham, Peter J Surg Case Rep Case Report Malignant inflammatory myofibroblastic tumors (IMT) are extremely rare, aggressive tumors with variable presentation. This is a case of a 29-year-old female presented with severe anemia and a large abdominal mass presumed to be a gastrointestinal stromal tumor (GIST). Severe anemia, leukocytosis and thrombocytosis accompanied the presentation. Final pathological assessment yielded a diagnosis of malignant IMT. Given the rarity of these tumors, no established diagnostic criteria exist aside from histological analysis of the tissue, which may result in delays or inappropriate treatment. As these tumors are aggressive in nature, a high index of suspicion is critical to improve outcomes. Further reports on the presentation, diagnosis and treatment of such rare tumors are important to develop clinical diagnostic guidelines to improve diagnosis and treatment and improve outcomes. Oxford University Press 2022-09-19 /pmc/articles/PMC9487198/ /pubmed/36148141 http://dx.doi.org/10.1093/jscr/rjac403 Text en Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2022. https://creativecommons.org/licenses/by/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted reuse, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Spafford, Megan
Lunn, Danley
Graham, Peter
Malignant inflammatory myofibroblastic tumor: a rare case presentation
title Malignant inflammatory myofibroblastic tumor: a rare case presentation
title_full Malignant inflammatory myofibroblastic tumor: a rare case presentation
title_fullStr Malignant inflammatory myofibroblastic tumor: a rare case presentation
title_full_unstemmed Malignant inflammatory myofibroblastic tumor: a rare case presentation
title_short Malignant inflammatory myofibroblastic tumor: a rare case presentation
title_sort malignant inflammatory myofibroblastic tumor: a rare case presentation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9487198/
https://www.ncbi.nlm.nih.gov/pubmed/36148141
http://dx.doi.org/10.1093/jscr/rjac403
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