Cargando…
Malignant inflammatory myofibroblastic tumor: a rare case presentation
Malignant inflammatory myofibroblastic tumors (IMT) are extremely rare, aggressive tumors with variable presentation. This is a case of a 29-year-old female presented with severe anemia and a large abdominal mass presumed to be a gastrointestinal stromal tumor (GIST). Severe anemia, leukocytosis and...
Autores principales: | , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2022
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9487198/ https://www.ncbi.nlm.nih.gov/pubmed/36148141 http://dx.doi.org/10.1093/jscr/rjac403 |
_version_ | 1784792442387562496 |
---|---|
author | Spafford, Megan Lunn, Danley Graham, Peter |
author_facet | Spafford, Megan Lunn, Danley Graham, Peter |
author_sort | Spafford, Megan |
collection | PubMed |
description | Malignant inflammatory myofibroblastic tumors (IMT) are extremely rare, aggressive tumors with variable presentation. This is a case of a 29-year-old female presented with severe anemia and a large abdominal mass presumed to be a gastrointestinal stromal tumor (GIST). Severe anemia, leukocytosis and thrombocytosis accompanied the presentation. Final pathological assessment yielded a diagnosis of malignant IMT. Given the rarity of these tumors, no established diagnostic criteria exist aside from histological analysis of the tissue, which may result in delays or inappropriate treatment. As these tumors are aggressive in nature, a high index of suspicion is critical to improve outcomes. Further reports on the presentation, diagnosis and treatment of such rare tumors are important to develop clinical diagnostic guidelines to improve diagnosis and treatment and improve outcomes. |
format | Online Article Text |
id | pubmed-9487198 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-94871982022-09-21 Malignant inflammatory myofibroblastic tumor: a rare case presentation Spafford, Megan Lunn, Danley Graham, Peter J Surg Case Rep Case Report Malignant inflammatory myofibroblastic tumors (IMT) are extremely rare, aggressive tumors with variable presentation. This is a case of a 29-year-old female presented with severe anemia and a large abdominal mass presumed to be a gastrointestinal stromal tumor (GIST). Severe anemia, leukocytosis and thrombocytosis accompanied the presentation. Final pathological assessment yielded a diagnosis of malignant IMT. Given the rarity of these tumors, no established diagnostic criteria exist aside from histological analysis of the tissue, which may result in delays or inappropriate treatment. As these tumors are aggressive in nature, a high index of suspicion is critical to improve outcomes. Further reports on the presentation, diagnosis and treatment of such rare tumors are important to develop clinical diagnostic guidelines to improve diagnosis and treatment and improve outcomes. Oxford University Press 2022-09-19 /pmc/articles/PMC9487198/ /pubmed/36148141 http://dx.doi.org/10.1093/jscr/rjac403 Text en Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2022. https://creativecommons.org/licenses/by/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted reuse, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Spafford, Megan Lunn, Danley Graham, Peter Malignant inflammatory myofibroblastic tumor: a rare case presentation |
title | Malignant inflammatory myofibroblastic tumor: a rare case presentation |
title_full | Malignant inflammatory myofibroblastic tumor: a rare case presentation |
title_fullStr | Malignant inflammatory myofibroblastic tumor: a rare case presentation |
title_full_unstemmed | Malignant inflammatory myofibroblastic tumor: a rare case presentation |
title_short | Malignant inflammatory myofibroblastic tumor: a rare case presentation |
title_sort | malignant inflammatory myofibroblastic tumor: a rare case presentation |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9487198/ https://www.ncbi.nlm.nih.gov/pubmed/36148141 http://dx.doi.org/10.1093/jscr/rjac403 |
work_keys_str_mv | AT spaffordmegan malignantinflammatorymyofibroblastictumorararecasepresentation AT lunndanley malignantinflammatorymyofibroblastictumorararecasepresentation AT grahampeter malignantinflammatorymyofibroblastictumorararecasepresentation |