Systematic review of drug effects in humans and models with surfactant-processing disease

Fibrotic interstitial pneumonias are a group of rare diseases characterised by distortion of lung interstitium. Patients with mutations in surfactant-processing genes, such as surfactant protein C (SFTPC), surfactant protein A1 and A2 (SFTPA1 and A2), ATP binding cassette A3 (ABCA3) and Hermansky–Pu...

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Detalles Bibliográficos
Autores principales: Klay, Dymph, Hoffman, Thijs W., Harmsze, Ankie M., Grutters, Jan C., van Moorsel, Coline H.M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2018
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9489115/
https://www.ncbi.nlm.nih.gov/pubmed/29997245
http://dx.doi.org/10.1183/16000617.0135-2017

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9489115/
https://www.ncbi.nlm.nih.gov/pubmed/29997245
http://dx.doi.org/10.1183/16000617.0135-2017

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