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Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intell...

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Detalles Bibliográficos
Autores principales: Zhang, Ying, Geng, Zhiyu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9510600/
https://www.ncbi.nlm.nih.gov/pubmed/36171814
http://dx.doi.org/10.3389/fsurg.2022.997162
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author Zhang, Ying
Geng, Zhiyu
author_facet Zhang, Ying
Geng, Zhiyu
author_sort Zhang, Ying
collection PubMed
description Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intellectual disability, and autonomic nervous system abnormalities. The clinical features may intrinsically pose anesthetic challenges. We present a case of a patient with CIPA who underwent tumor biopsy under general anesthesia using a Supreme laryngeal mask airway without any complications. The anesthetic management of this condition is discussed.
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spelling pubmed-95106002022-09-27 Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report Zhang, Ying Geng, Zhiyu Front Surg Surgery Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intellectual disability, and autonomic nervous system abnormalities. The clinical features may intrinsically pose anesthetic challenges. We present a case of a patient with CIPA who underwent tumor biopsy under general anesthesia using a Supreme laryngeal mask airway without any complications. The anesthetic management of this condition is discussed. Frontiers Media S.A. 2022-09-12 /pmc/articles/PMC9510600/ /pubmed/36171814 http://dx.doi.org/10.3389/fsurg.2022.997162 Text en © 2022 Zhang and Geng. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY) (https://creativecommons.org/licenses/by/4.0/) . The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Surgery
Zhang, Ying
Geng, Zhiyu
Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
title Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
title_full Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
title_fullStr Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
title_full_unstemmed Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
title_short Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
title_sort anesthetic management of a child with congenital insensitivity to pain with anhidrosis: a case report
topic Surgery
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9510600/
https://www.ncbi.nlm.nih.gov/pubmed/36171814
http://dx.doi.org/10.3389/fsurg.2022.997162
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