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Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intell...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Frontiers Media S.A.
2022
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9510600/ https://www.ncbi.nlm.nih.gov/pubmed/36171814 http://dx.doi.org/10.3389/fsurg.2022.997162 |
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author | Zhang, Ying Geng, Zhiyu |
author_facet | Zhang, Ying Geng, Zhiyu |
author_sort | Zhang, Ying |
collection | PubMed |
description | Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intellectual disability, and autonomic nervous system abnormalities. The clinical features may intrinsically pose anesthetic challenges. We present a case of a patient with CIPA who underwent tumor biopsy under general anesthesia using a Supreme laryngeal mask airway without any complications. The anesthetic management of this condition is discussed. |
format | Online Article Text |
id | pubmed-9510600 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Frontiers Media S.A. |
record_format | MEDLINE/PubMed |
spelling | pubmed-95106002022-09-27 Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report Zhang, Ying Geng, Zhiyu Front Surg Surgery Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intellectual disability, and autonomic nervous system abnormalities. The clinical features may intrinsically pose anesthetic challenges. We present a case of a patient with CIPA who underwent tumor biopsy under general anesthesia using a Supreme laryngeal mask airway without any complications. The anesthetic management of this condition is discussed. Frontiers Media S.A. 2022-09-12 /pmc/articles/PMC9510600/ /pubmed/36171814 http://dx.doi.org/10.3389/fsurg.2022.997162 Text en © 2022 Zhang and Geng. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY) (https://creativecommons.org/licenses/by/4.0/) . The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms. |
spellingShingle | Surgery Zhang, Ying Geng, Zhiyu Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report |
title | Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report |
title_full | Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report |
title_fullStr | Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report |
title_full_unstemmed | Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report |
title_short | Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report |
title_sort | anesthetic management of a child with congenital insensitivity to pain with anhidrosis: a case report |
topic | Surgery |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9510600/ https://www.ncbi.nlm.nih.gov/pubmed/36171814 http://dx.doi.org/10.3389/fsurg.2022.997162 |
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