Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma

Extra-gastrointestinal stromal tumors (EGISTs) are rare mesenchymal tumors accounting for less than 1% of total gastrointestinal tumors. They tend to be aggressive and have a poor prognosis. Unfortunately, there is a lack of data or controversial data due to its scarcity. Therefore, we report a case...

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Autores principales: El-Helou, Etienne, Chamma, Linda, Mazraani, Houssam Bashir, Sebaaly, Delivrance, Chamma, Omar Georges, Naccour, Jessica, Haddad, Marwan M., Lichaa, Dani, Alam, Houssam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Medical Publishers, Inc. 2022
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9512592/
https://www.ncbi.nlm.nih.gov/pubmed/36172533
http://dx.doi.org/10.1055/s-0042-1757335
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author El-Helou, Etienne
Chamma, Linda
Mazraani, Houssam Bashir
Sebaaly, Delivrance
Chamma, Omar Georges
Naccour, Jessica
Haddad, Marwan M.
Lichaa, Dani
Alam, Houssam
author_facet El-Helou, Etienne
Chamma, Linda
Mazraani, Houssam Bashir
Sebaaly, Delivrance
Chamma, Omar Georges
Naccour, Jessica
Haddad, Marwan M.
Lichaa, Dani
Alam, Houssam
author_sort El-Helou, Etienne
collection PubMed
description Extra-gastrointestinal stromal tumors (EGISTs) are rare mesenchymal tumors accounting for less than 1% of total gastrointestinal tumors. They tend to be aggressive and have a poor prognosis. Unfortunately, there is a lack of data or controversial data due to its scarcity. Therefore, we report a case of pelvic EGIST misdiagnosed as retroperitoneal sarcoma. We opted for surgical management followed by adjuvant oral chemotherapy with imatinib.
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spelling pubmed-95125922022-09-27 Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma El-Helou, Etienne Chamma, Linda Mazraani, Houssam Bashir Sebaaly, Delivrance Chamma, Omar Georges Naccour, Jessica Haddad, Marwan M. Lichaa, Dani Alam, Houssam Surg J (N Y) Extra-gastrointestinal stromal tumors (EGISTs) are rare mesenchymal tumors accounting for less than 1% of total gastrointestinal tumors. They tend to be aggressive and have a poor prognosis. Unfortunately, there is a lack of data or controversial data due to its scarcity. Therefore, we report a case of pelvic EGIST misdiagnosed as retroperitoneal sarcoma. We opted for surgical management followed by adjuvant oral chemotherapy with imatinib. Thieme Medical Publishers, Inc. 2022-09-26 /pmc/articles/PMC9512592/ /pubmed/36172533 http://dx.doi.org/10.1055/s-0042-1757335 Text en The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. ( https://creativecommons.org/licenses/by/4.0/ ) https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle El-Helou, Etienne
Chamma, Linda
Mazraani, Houssam Bashir
Sebaaly, Delivrance
Chamma, Omar Georges
Naccour, Jessica
Haddad, Marwan M.
Lichaa, Dani
Alam, Houssam
Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma
title Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma
title_full Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma
title_fullStr Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma
title_full_unstemmed Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma
title_short Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma
title_sort extra-gastrointestinal stromal tumor (egist) in the pelvis mimicking retroperitoneal sarcoma
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9512592/
https://www.ncbi.nlm.nih.gov/pubmed/36172533
http://dx.doi.org/10.1055/s-0042-1757335
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