Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases

Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic g...

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Detalles Bibliográficos
Autores principales: Basu, Suprit, Tyagi, Reva, Jindal, Ankur Kumar, Medha, Apurva, Banday, Aaqib Zaffar, Babbar, Alisha, Sharma, Apoorva, Mahajan, Rahul, Vignesh, Pandiarajan, Rawat, Amit
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Pediatrics
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9530593/
https://www.ncbi.nlm.nih.gov/pubmed/36204672
http://dx.doi.org/10.3389/fped.2022.953033
Descripción
Sumario:Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic granulomatous disease (CGD) has not been reported previously. Here, we report 2 cases of liver abscess in PLS that responded to corticosteroids.

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