Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases

Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic g...

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Autores principales: Basu, Suprit, Tyagi, Reva, Jindal, Ankur Kumar, Medha, Apurva, Banday, Aaqib Zaffar, Babbar, Alisha, Sharma, Apoorva, Mahajan, Rahul, Vignesh, Pandiarajan, Rawat, Amit
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Pediatrics
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9530593/
https://www.ncbi.nlm.nih.gov/pubmed/36204672
http://dx.doi.org/10.3389/fped.2022.953033
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author Basu, Suprit
Tyagi, Reva
Jindal, Ankur Kumar
Medha, Apurva
Banday, Aaqib Zaffar
Babbar, Alisha
Sharma, Apoorva
Mahajan, Rahul
Vignesh, Pandiarajan
Rawat, Amit
author_facet Basu, Suprit
Tyagi, Reva
Jindal, Ankur Kumar
Medha, Apurva
Banday, Aaqib Zaffar
Babbar, Alisha
Sharma, Apoorva
Mahajan, Rahul
Vignesh, Pandiarajan
Rawat, Amit
author_sort Basu, Suprit
collection PubMed
description Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic granulomatous disease (CGD) has not been reported previously. Here, we report 2 cases of liver abscess in PLS that responded to corticosteroids.
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spelling pubmed-95305932022-10-05 Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases Basu, Suprit Tyagi, Reva Jindal, Ankur Kumar Medha, Apurva Banday, Aaqib Zaffar Babbar, Alisha Sharma, Apoorva Mahajan, Rahul Vignesh, Pandiarajan Rawat, Amit Front Pediatr Pediatrics Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic granulomatous disease (CGD) has not been reported previously. Here, we report 2 cases of liver abscess in PLS that responded to corticosteroids. Frontiers Media S.A. 2022-09-20 /pmc/articles/PMC9530593/ /pubmed/36204672 http://dx.doi.org/10.3389/fped.2022.953033 Text en Copyright © 2022 Basu, Tyagi, Jindal, Medha, Banday, Babbar, Sharma, Mahajan, Vignesh and Rawat. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Pediatrics
Basu, Suprit
Tyagi, Reva
Jindal, Ankur Kumar
Medha, Apurva
Banday, Aaqib Zaffar
Babbar, Alisha
Sharma, Apoorva
Mahajan, Rahul
Vignesh, Pandiarajan
Rawat, Amit
Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
title Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
title_full Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
title_fullStr Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
title_full_unstemmed Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
title_short Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
title_sort case report: corticosteroids as an adjunct treatment for the management of liver abscess in papillon–lefèvre syndrome: a report on two cases
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9530593/
https://www.ncbi.nlm.nih.gov/pubmed/36204672
http://dx.doi.org/10.3389/fped.2022.953033
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