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Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene

Acute promyelocytic leukemia (APL) is characterized by the balanced translocation of chromosomes 15 and 17, resulting in the formation of PML-RARA fusion gene. More than 98% of APL have PML-RARA fusion, and less than 2% have other types of RARA gene partners, which named variant APL (vAPL). In the p...

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Autores principales: Chen, Li, Zhu, Hongming, Zhu, Yongmei, Jin, Wen, Dong, Fangyi, Li, Jianfeng, Hu, Jiong, Chen, Qiusheng, Wang, Kankan, Li, Junmin
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9539026/
https://www.ncbi.nlm.nih.gov/pubmed/36212492
http://dx.doi.org/10.3389/fonc.2022.1013046
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author Chen, Li
Zhu, Hongming
Zhu, Yongmei
Jin, Wen
Dong, Fangyi
Li, Jianfeng
Hu, Jiong
Chen, Qiusheng
Wang, Kankan
Li, Junmin
author_facet Chen, Li
Zhu, Hongming
Zhu, Yongmei
Jin, Wen
Dong, Fangyi
Li, Jianfeng
Hu, Jiong
Chen, Qiusheng
Wang, Kankan
Li, Junmin
author_sort Chen, Li
collection PubMed
description Acute promyelocytic leukemia (APL) is characterized by the balanced translocation of chromosomes 15 and 17, resulting in the formation of PML-RARA fusion gene. More than 98% of APL have PML-RARA fusion, and less than 2% have other types of RARA gene partners, which named variant APL (vAPL). In the present study, we reported a vAPL with BCOR-RARA, which was the third case of BCOR-RARA APL published. The patient achieved complete remission (CR) with all-trans retinoic acid (ATRA) monotherapy, and molecular CR with ATRA plus standard chemotherapy. After that, he underwent allogeneic hematopoietic stem cell transplantation (allo-HSCT) and ATRA maintenance and maintained a molecular CR status. This case provided valuable insights into the accurate identification of vAPL. Moreover, ATRA combined with chemotherapy followed by allo-HSCT was suggested as an optimal choice for those vAPL patients who had a high risk of relapse.
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spelling pubmed-95390262022-10-08 Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene Chen, Li Zhu, Hongming Zhu, Yongmei Jin, Wen Dong, Fangyi Li, Jianfeng Hu, Jiong Chen, Qiusheng Wang, Kankan Li, Junmin Front Oncol Oncology Acute promyelocytic leukemia (APL) is characterized by the balanced translocation of chromosomes 15 and 17, resulting in the formation of PML-RARA fusion gene. More than 98% of APL have PML-RARA fusion, and less than 2% have other types of RARA gene partners, which named variant APL (vAPL). In the present study, we reported a vAPL with BCOR-RARA, which was the third case of BCOR-RARA APL published. The patient achieved complete remission (CR) with all-trans retinoic acid (ATRA) monotherapy, and molecular CR with ATRA plus standard chemotherapy. After that, he underwent allogeneic hematopoietic stem cell transplantation (allo-HSCT) and ATRA maintenance and maintained a molecular CR status. This case provided valuable insights into the accurate identification of vAPL. Moreover, ATRA combined with chemotherapy followed by allo-HSCT was suggested as an optimal choice for those vAPL patients who had a high risk of relapse. Frontiers Media S.A. 2022-09-23 /pmc/articles/PMC9539026/ /pubmed/36212492 http://dx.doi.org/10.3389/fonc.2022.1013046 Text en Copyright © 2022 Chen, Zhu, Zhu, Jin, Dong, Li, Hu, Chen, Wang and Li https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Oncology
Chen, Li
Zhu, Hongming
Zhu, Yongmei
Jin, Wen
Dong, Fangyi
Li, Jianfeng
Hu, Jiong
Chen, Qiusheng
Wang, Kankan
Li, Junmin
Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene
title Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene
title_full Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene
title_fullStr Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene
title_full_unstemmed Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene
title_short Case Report: Successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the BCOR-RARA fusion gene
title_sort case report: successful therapy with all-trans retinoic acid combined with chemotherapy followed by hematopoietic stem cell transplantation for acute promyelocytic leukemia carrying the bcor-rara fusion gene
topic Oncology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9539026/
https://www.ncbi.nlm.nih.gov/pubmed/36212492
http://dx.doi.org/10.3389/fonc.2022.1013046
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