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Double Valve Replacement in a Patient With Hunter Syndrome

Hunter syndrome is a rare disorder in which affected patients have significant airway abnormalities (macroglossia, small mouth opening, and supraglottic narrowing) that complicate their management. Deposition of glycosaminoglycans in the heart leads to cardiomyopathy, and cardiac valve dysplasia tha...

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Detalles Bibliográficos
Autores principales: Keshavamurthy, Suresh, Duncan, Andra, Kumar, Akshay, Trombetta, Carlos, Rodriguez, Rene, Tan, Carmela, Roselli, Eric
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9547770/
https://www.ncbi.nlm.nih.gov/pubmed/36237781
http://dx.doi.org/10.7759/cureus.28961
Descripción
Sumario:Hunter syndrome is a rare disorder in which affected patients have significant airway abnormalities (macroglossia, small mouth opening, and supraglottic narrowing) that complicate their management. Deposition of glycosaminoglycans in the heart leads to cardiomyopathy, and cardiac valve dysplasia that can lead to valvular stenosis or regurgitation or both, necessitating valve replacement. Management of patients with Hunter syndrome is complex and needs a multidisciplinary team approach. Mechanical valve replacement is a suitable treatment option.