Double Valve Replacement in a Patient With Hunter Syndrome

Hunter syndrome is a rare disorder in which affected patients have significant airway abnormalities (macroglossia, small mouth opening, and supraglottic narrowing) that complicate their management. Deposition of glycosaminoglycans in the heart leads to cardiomyopathy, and cardiac valve dysplasia tha...

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Detalles Bibliográficos
Autores principales: Keshavamurthy, Suresh, Duncan, Andra, Kumar, Akshay, Trombetta, Carlos, Rodriguez, Rene, Tan, Carmela, Roselli, Eric
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Cardiac/Thoracic/Vascular Surgery
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9547770/
https://www.ncbi.nlm.nih.gov/pubmed/36237781
http://dx.doi.org/10.7759/cureus.28961
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author Keshavamurthy, Suresh
Duncan, Andra
Kumar, Akshay
Trombetta, Carlos
Rodriguez, Rene
Tan, Carmela
Roselli, Eric
author_facet Keshavamurthy, Suresh
Duncan, Andra
Kumar, Akshay
Trombetta, Carlos
Rodriguez, Rene
Tan, Carmela
Roselli, Eric
author_sort Keshavamurthy, Suresh
collection PubMed
description Hunter syndrome is a rare disorder in which affected patients have significant airway abnormalities (macroglossia, small mouth opening, and supraglottic narrowing) that complicate their management. Deposition of glycosaminoglycans in the heart leads to cardiomyopathy, and cardiac valve dysplasia that can lead to valvular stenosis or regurgitation or both, necessitating valve replacement. Management of patients with Hunter syndrome is complex and needs a multidisciplinary team approach. Mechanical valve replacement is a suitable treatment option.
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spelling pubmed-95477702022-10-12 Double Valve Replacement in a Patient With Hunter Syndrome Keshavamurthy, Suresh Duncan, Andra Kumar, Akshay Trombetta, Carlos Rodriguez, Rene Tan, Carmela Roselli, Eric Cureus Cardiac/Thoracic/Vascular Surgery Hunter syndrome is a rare disorder in which affected patients have significant airway abnormalities (macroglossia, small mouth opening, and supraglottic narrowing) that complicate their management. Deposition of glycosaminoglycans in the heart leads to cardiomyopathy, and cardiac valve dysplasia that can lead to valvular stenosis or regurgitation or both, necessitating valve replacement. Management of patients with Hunter syndrome is complex and needs a multidisciplinary team approach. Mechanical valve replacement is a suitable treatment option. Cureus 2022-09-08 /pmc/articles/PMC9547770/ /pubmed/36237781 http://dx.doi.org/10.7759/cureus.28961 Text en Copyright © 2022, Keshavamurthy et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Cardiac/Thoracic/Vascular Surgery
Keshavamurthy, Suresh
Duncan, Andra
Kumar, Akshay
Trombetta, Carlos
Rodriguez, Rene
Tan, Carmela
Roselli, Eric
Double Valve Replacement in a Patient With Hunter Syndrome
title Double Valve Replacement in a Patient With Hunter Syndrome
title_full Double Valve Replacement in a Patient With Hunter Syndrome
title_fullStr Double Valve Replacement in a Patient With Hunter Syndrome
title_full_unstemmed Double Valve Replacement in a Patient With Hunter Syndrome
title_short Double Valve Replacement in a Patient With Hunter Syndrome
title_sort double valve replacement in a patient with hunter syndrome
topic Cardiac/Thoracic/Vascular Surgery
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9547770/
https://www.ncbi.nlm.nih.gov/pubmed/36237781
http://dx.doi.org/10.7759/cureus.28961
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