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Exploring the impact of elexacaftor-tezacaftor-ivacaftor treatment on opinions regarding airway clearance techniques and nebulisers: TEMPO a qualitative study in children with cystic fibrosis, their families and healthcare professionals

BACKGROUND: Cystic fibrosis (CF) is a genetic condition caused by variants in the cystic fibrosis transmembrane conductance regulator (CFTR) gene that primarily impacts the lungs. Treatments historically have been symptomatic to improve airway clearance and treat infection. However, CFTR modulator d...

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Detalles Bibliográficos
Autores principales:	Almulhem, Maryam, Harnett, Nuala, Graham, Stephanie, Haq, Iram, Visram, Shelina, Ward, Christopher, Brodlie, Malcolm
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BMJ Publishing Group 2022
Materias:	Cystic Fibrosis
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9557266/ https://www.ncbi.nlm.nih.gov/pubmed/36207030 http://dx.doi.org/10.1136/bmjresp-2022-001420

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