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An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient
The Duke–Davidoff–Masson syndrome (DDMS) is a rare neurological condition with unknown prevalence, globally. To date, <100 cases have been reported worldwide. We report the case of an 18‐year‐old patient admitted for status epilepticus seizure, and who presented a right hemiparesis, body asymmetr...
Autores principales: | , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9576958/ https://www.ncbi.nlm.nih.gov/pubmed/36267824 http://dx.doi.org/10.1002/ccr3.6428 |
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author | Djimdé, Samba O. Yalcouyé, Abdoulaye Koïta, Abdou Samir, Hassana Kebkiba, Pofinet Gueli, Chrystelle Awovi Maïga, Alassane B. Sissoko, Adama S. Landouré, Guida |
author_facet | Djimdé, Samba O. Yalcouyé, Abdoulaye Koïta, Abdou Samir, Hassana Kebkiba, Pofinet Gueli, Chrystelle Awovi Maïga, Alassane B. Sissoko, Adama S. Landouré, Guida |
author_sort | Djimdé, Samba O. |
collection | PubMed |
description | The Duke–Davidoff–Masson syndrome (DDMS) is a rare neurological condition with unknown prevalence, globally. To date, <100 cases have been reported worldwide. We report the case of an 18‐year‐old patient admitted for status epilepticus seizure, and who presented a right hemiparesis, body asymmetry, joints ankylosis, and mental retardation. Brain CT‐scan revealed left hemisphere atrophy, skull bone thickening, and hyperpneumatization of the frontal sinuses; all consistent with DDMS. Seizures improved remarkably on Levetiracetam and Valproate. This is the first report of an unusual DDMS in Mali, and the diagnosis delay highlights the challenges for the management of these diseases in resource‐limited settings. |
format | Online Article Text |
id | pubmed-9576958 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | John Wiley and Sons Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-95769582022-10-19 An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient Djimdé, Samba O. Yalcouyé, Abdoulaye Koïta, Abdou Samir, Hassana Kebkiba, Pofinet Gueli, Chrystelle Awovi Maïga, Alassane B. Sissoko, Adama S. Landouré, Guida Clin Case Rep Case Report The Duke–Davidoff–Masson syndrome (DDMS) is a rare neurological condition with unknown prevalence, globally. To date, <100 cases have been reported worldwide. We report the case of an 18‐year‐old patient admitted for status epilepticus seizure, and who presented a right hemiparesis, body asymmetry, joints ankylosis, and mental retardation. Brain CT‐scan revealed left hemisphere atrophy, skull bone thickening, and hyperpneumatization of the frontal sinuses; all consistent with DDMS. Seizures improved remarkably on Levetiracetam and Valproate. This is the first report of an unusual DDMS in Mali, and the diagnosis delay highlights the challenges for the management of these diseases in resource‐limited settings. John Wiley and Sons Inc. 2022-10-17 /pmc/articles/PMC9576958/ /pubmed/36267824 http://dx.doi.org/10.1002/ccr3.6428 Text en © 2022 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made. |
spellingShingle | Case Report Djimdé, Samba O. Yalcouyé, Abdoulaye Koïta, Abdou Samir, Hassana Kebkiba, Pofinet Gueli, Chrystelle Awovi Maïga, Alassane B. Sissoko, Adama S. Landouré, Guida An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient |
title | An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient |
title_full | An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient |
title_fullStr | An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient |
title_full_unstemmed | An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient |
title_short | An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient |
title_sort | unusual case of dyke–davidoff–masson syndrome revealed by status epilepticus in a malian patient |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9576958/ https://www.ncbi.nlm.nih.gov/pubmed/36267824 http://dx.doi.org/10.1002/ccr3.6428 |
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