Transition from paediatric to adult care in cystic fibrosis

In the decades since cystic fibrosis (CF) was first clinically defined in the 1930s, there have been many advancements in the treatment and management of this disease. Initially it was considered a disease of childhood where the majority of those affected died before reaching adolescence. Now, through advancements in management and treatment, the vast majority of those affected will live into adulthood. Therefore, paediatric and adult CF services must collaborate to ensure that young people and their families experience a positive and supportive transition into adult services. Key aspects of transition will be discussed, including when to begin the transition process, who should coordinate this and how the transition process should be structured. Challenges of the transition process and potential pitfalls when transition does not run smoothly will also be discussed, as well as tools that may be used to support a positive transition for young people and their families. EDUCATIONAL AIMS: To familiarise readers with factors that make the transition process positive. To make suggestions regarding the application of the transition process. To highlight factors which may impact on the success of the transition process and the risks associated with disengagement at the point of transition. To discuss tools which can be used by care teams to ensure a smooth transition process.