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Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report

Neuromyelitis optica spectrum disease (NMOSD) is a debilitating autoimmune inflammatory demyelinating disease of the central nervous system. The relationship between harboring an infection and NMOSD is currently unclear and needs further investigation. This article reports meningoencephalitis-like m...

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Autores principales: Bu, Yi, Liu, Heng, Qian, XuDong, Sun, Fan, Li, ChengBo, Han, Jingzhe
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9585379/
https://www.ncbi.nlm.nih.gov/pubmed/36275714
http://dx.doi.org/10.3389/fimmu.2022.938492
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author Bu, Yi
Liu, Heng
Qian, XuDong
Sun, Fan
Li, ChengBo
Han, Jingzhe
author_facet Bu, Yi
Liu, Heng
Qian, XuDong
Sun, Fan
Li, ChengBo
Han, Jingzhe
author_sort Bu, Yi
collection PubMed
description Neuromyelitis optica spectrum disease (NMOSD) is a debilitating autoimmune inflammatory demyelinating disease of the central nervous system. The relationship between harboring an infection and NMOSD is currently unclear and needs further investigation. This article reports meningoencephalitis-like manifestations, including fever, headache, neck resistance, seizures, and pleocytosis, accompanied by nausea and vomiting, in a patient with serum AQP4 antibody-positive area postrema syndrome (APS). In the presence of aseptic meningitis combined with clinical symptoms such as optic neuritis and myelitis, the possibility of NMOSD diagnosis can be considered. However, for patients with unknown causes, especially combined with aseptic meningitis, a probable differential diagnosis of NMOSD is considered.
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spelling pubmed-95853792022-10-22 Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report Bu, Yi Liu, Heng Qian, XuDong Sun, Fan Li, ChengBo Han, Jingzhe Front Immunol Immunology Neuromyelitis optica spectrum disease (NMOSD) is a debilitating autoimmune inflammatory demyelinating disease of the central nervous system. The relationship between harboring an infection and NMOSD is currently unclear and needs further investigation. This article reports meningoencephalitis-like manifestations, including fever, headache, neck resistance, seizures, and pleocytosis, accompanied by nausea and vomiting, in a patient with serum AQP4 antibody-positive area postrema syndrome (APS). In the presence of aseptic meningitis combined with clinical symptoms such as optic neuritis and myelitis, the possibility of NMOSD diagnosis can be considered. However, for patients with unknown causes, especially combined with aseptic meningitis, a probable differential diagnosis of NMOSD is considered. Frontiers Media S.A. 2022-10-06 /pmc/articles/PMC9585379/ /pubmed/36275714 http://dx.doi.org/10.3389/fimmu.2022.938492 Text en Copyright © 2022 Bu, Liu, Qian, Sun, Li and Han https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Immunology
Bu, Yi
Liu, Heng
Qian, XuDong
Sun, Fan
Li, ChengBo
Han, Jingzhe
Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report
title Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report
title_full Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report
title_fullStr Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report
title_full_unstemmed Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report
title_short Aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: A case report
title_sort aquaporin 4-positive neuromyelitis optica spectrum disorder with meningoencephalitis-like onset: a case report
topic Immunology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9585379/
https://www.ncbi.nlm.nih.gov/pubmed/36275714
http://dx.doi.org/10.3389/fimmu.2022.938492
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