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Nintedanib Reduces Muscle Fibrosis and Improves Muscle Function of the Alpha-Sarcoglycan-Deficient Mice

Sarcoglycanopathies are a group of recessive limb-girdle muscular dystrophies, characterized by progressive muscle weakness. Sarcoglycan deficiency produces instability of the sarcolemma during muscle contraction, leading to continuous muscle fiber injury eventually producing fiber loss and replacem...

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Detalles Bibliográficos
Autores principales:	Alonso-Pérez, Jorge, Carrasco-Rozas, Ana, Borrell-Pages, Maria, Fernández-Simón, Esther, Piñol-Jurado, Patricia, Badimon, Lina, Wollin, Lutz, Lleixà, Cinta, Gallardo, Eduard, Olivé, Montse, Díaz-Manera, Jordi, Suárez-Calvet, Xavier
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9599168/ https://www.ncbi.nlm.nih.gov/pubmed/36289891 http://dx.doi.org/10.3390/biomedicines10102629

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