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Stimulating Mitochondrial Biogenesis with Deoxyribonucleosides Increases Functional Capacity in ECHS1-Deficient Cells
The lack of effective treatments for mitochondrial disease has seen the development of new approaches, including those that stimulate mitochondrial biogenesis to boost ATP production. Here, we examined the effects of deoxyribonucleosides (dNs) on mitochondrial biogenesis and function in Short chain...
Autores principales: | Burgin, Harrison James, Crameri, Jordan James, Stojanovski, Diana, Sanchez, M. Isabel G. Lopez, Ziemann, Mark, McKenzie, Matthew |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9604038/ https://www.ncbi.nlm.nih.gov/pubmed/36293464 http://dx.doi.org/10.3390/ijms232012610 |
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