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Impact of CFTR Modulators on the Impaired Function of Phagocytes in Cystic Fibrosis Lung Disease
Cystic fibrosis (CF), the most common genetically inherited disease in Caucasian populations, is a multi-systemic life-threatening autosomal recessive disorder caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. In 2012, the arrival of CFTR modulators (potenti...
Autores principales: | Meoli, Aniello, Eickmeier, Olaf, Pisi, Giovanna, Fainardi, Valentina, Zielen, Stefan, Esposito, Susanna |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9604330/ https://www.ncbi.nlm.nih.gov/pubmed/36293274 http://dx.doi.org/10.3390/ijms232012421 |
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