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Evidence of protective effects of recombinant ADAMTS13 in a humanized model of sickle cell disease

Sickle cell disease (SCD) is an inherited red blood cell disorder that occurs worldwide. Acute vaso-occlusive crisis is the main cause of hospitalization in patients with SCD. There is growing evidence that inflammatory vasculopathy plays a key role in both acute and chronic SCD-related clinical man...

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Detalles Bibliográficos
Autores principales:	Rossato, Paolo, Federti, Enrica, Matte’, Alessandro, Glantschnig, Helmut, Canneva, Fabio, Schuster, Maria, Coulibaly, Sogue, Schrenk, Gerald, Voelkel, Dirk, Dockal, Michael, Plaimauer, Barbara, Andolfo, Immacolata, Iolascon, Achille, Rottensteiner, Hanspeter, Gritsch, Herbert, Scheiflinger, Friedrich, Hoellriegl, Werner, De Franceschi, Lucia
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Fondazione Ferrata Storti 2022
Materias:	Article - Coagulation & its Disorders
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9614531/ https://www.ncbi.nlm.nih.gov/pubmed/35443560 http://dx.doi.org/10.3324/haematol.2021.280233

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