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Arrhythmogenic Cardiomyopathy: A Review of a Rare Case of Biventricular Phenotype

Arrhythmogenic cardiomyopathy is a rare hereditary structural heart disease, with various phenotypes, which mostly affects the right ventricle of the heart, resulting in fibrofatty replacement of the heart muscles and a proclivity to create spontaneous malignant cardiac arrhythmias that may lead to...

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Detalles Bibliográficos
Autores principales: Aiwuyo, Henry O, Javed, Gulfam, Ataiyero, Omotomilola, Ibeson, Emeka C, Torere, Beatrice, Umuerri, Ejiro M, El Hadj Othmane, Taha
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9637405/
https://www.ncbi.nlm.nih.gov/pubmed/36381856
http://dx.doi.org/10.7759/cureus.30040
Descripción
Sumario:Arrhythmogenic cardiomyopathy is a rare hereditary structural heart disease, with various phenotypes, which mostly affects the right ventricle of the heart, resulting in fibrofatty replacement of the heart muscles and a proclivity to create spontaneous malignant cardiac arrhythmias that may lead to sudden death. Most previous reports were noted on young people. We report a case of its biventricular phenotype in a 61-year-old heavy truck driver who has a current medical history of diabetes mellitus and smoking and was incidentally diagnosed based on the Padua criteria after presenting to the hospital with complaints of lightheadedness and syncope. He eventually had an implantable cardioverter defibrillator, hence preventing death. We were able to correctly diagnose the case and prevent sudden cardiac death by instituting the necessary management.