Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa

WHAT IS ALREADY KNOWN ABOUT THIS TOPIC? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for b...

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Detalles Bibliográficos
Autores principales: Box, Rachel, Bernardis, Catina, Pleshkov, Alexander, Jessop, Nicky, Miller, Catherine, Skye, Jennifer, O’Brien, Virginia, Veerkamp, Matthew, da Rocha, Anna Carolina Ferreira, Cornwall, Roger
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2022
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9641806/
https://www.ncbi.nlm.nih.gov/pubmed/36345025
http://dx.doi.org/10.1186/s13023-022-02282-0
Descripción
Sumario:WHAT IS ALREADY KNOWN ABOUT THIS TOPIC? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. WHAT DOES THIS STUDY ADD? These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount. SUPPLEMENTARY INFORMATION: The online version contains supplementary material available at 10.1186/s13023-022-02282-0.

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