Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa

WHAT IS ALREADY KNOWN ABOUT THIS TOPIC? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for b...

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Autores principales: Box, Rachel, Bernardis, Catina, Pleshkov, Alexander, Jessop, Nicky, Miller, Catherine, Skye, Jennifer, O’Brien, Virginia, Veerkamp, Matthew, da Rocha, Anna Carolina Ferreira, Cornwall, Roger
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2022
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9641806/
https://www.ncbi.nlm.nih.gov/pubmed/36345025
http://dx.doi.org/10.1186/s13023-022-02282-0
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author Box, Rachel
Bernardis, Catina
Pleshkov, Alexander
Jessop, Nicky
Miller, Catherine
Skye, Jennifer
O’Brien, Virginia
Veerkamp, Matthew
da Rocha, Anna Carolina Ferreira
Cornwall, Roger
author_facet Box, Rachel
Bernardis, Catina
Pleshkov, Alexander
Jessop, Nicky
Miller, Catherine
Skye, Jennifer
O’Brien, Virginia
Veerkamp, Matthew
da Rocha, Anna Carolina Ferreira
Cornwall, Roger
author_sort Box, Rachel
collection PubMed
description WHAT IS ALREADY KNOWN ABOUT THIS TOPIC? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. WHAT DOES THIS STUDY ADD? These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount. SUPPLEMENTARY INFORMATION: The online version contains supplementary material available at 10.1186/s13023-022-02282-0.
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spelling pubmed-96418062022-11-15 Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa Box, Rachel Bernardis, Catina Pleshkov, Alexander Jessop, Nicky Miller, Catherine Skye, Jennifer O’Brien, Virginia Veerkamp, Matthew da Rocha, Anna Carolina Ferreira Cornwall, Roger Orphanet J Rare Dis Review WHAT IS ALREADY KNOWN ABOUT THIS TOPIC? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. WHAT DOES THIS STUDY ADD? These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount. SUPPLEMENTARY INFORMATION: The online version contains supplementary material available at 10.1186/s13023-022-02282-0. BioMed Central 2022-11-07 /pmc/articles/PMC9641806/ /pubmed/36345025 http://dx.doi.org/10.1186/s13023-022-02282-0 Text en © The Author(s) 2022 https://creativecommons.org/licenses/by/4.0/Open AccessThis article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) . The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/ (https://creativecommons.org/publicdomain/zero/1.0/) ) applies to the data made available in this article, unless otherwise stated in a credit line to the data.
spellingShingle Review
Box, Rachel
Bernardis, Catina
Pleshkov, Alexander
Jessop, Nicky
Miller, Catherine
Skye, Jennifer
O’Brien, Virginia
Veerkamp, Matthew
da Rocha, Anna Carolina Ferreira
Cornwall, Roger
Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
title Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
title_full Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
title_fullStr Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
title_full_unstemmed Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
title_short Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
title_sort hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9641806/
https://www.ncbi.nlm.nih.gov/pubmed/36345025
http://dx.doi.org/10.1186/s13023-022-02282-0
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