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Alveolar proteinosis of genetic origins

Pulmonary alveolar proteinosis (PAP) is a rare form of chronic interstitial lung disease, characterised by the intra-alveolar accumulation of lipoproteinaceous material. Numerous conditions can lead to its development. Whereas the autoimmune type is the main cause in adults, genetic defects account...

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Detalles Bibliográficos
Autores principales: Hadchouel, Alice, Drummond, David, Abou Taam, Rola, Lebourgeois, Muriel, Delacourt, Christophe, de Blic, Jacques
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9648510/
https://www.ncbi.nlm.nih.gov/pubmed/33115790
http://dx.doi.org/10.1183/16000617.0187-2019

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