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Comparison of quadriceps muscle size and quality in adults with cystic fibrosis with different severities of cystic fibrosis transmembrane conductance regulator protein dysfunction
BACKGROUND: Cystic fibrosis (CF) is characterized by CF transmembrane conductance regulator (CFTR) dysfunction. CFTR protein is expressed in human skeletal muscle; however, its impact on skeletal muscle is unknown. The objectives of this study were to compare quadriceps muscle size and quality betwe...
Autores principales: | Wu, Kenneth, Michalski, Anna, Sykes, Jenna, Batt, Jane, Stephenson, Anne L, Mathur, Sunita |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
SAGE Publications
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9669672/ https://www.ncbi.nlm.nih.gov/pubmed/36380568 http://dx.doi.org/10.1177/14799731221131330 |
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