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A Rare Case of Systemic Cystic Angiomatosis Involving the Bones, Spleen, Liver, and Lungs

Systemic cystic angiomatosis (SCA) is a rare disorder, usually involving the visceral organs with incidental detection during its insidious course. On radiography, it can present as multiple cystic lesions. In rare instances, it can present as mixed lesions (lytic, sclerotic) as was the case with ou...

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Detalles Bibliográficos
Autores principales: Sawalgi, Veda, Amin, Dhanush, Arora, Abhishek J, Srivastava, Madhur, Uppin, Megha
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9671484/
https://www.ncbi.nlm.nih.gov/pubmed/36407140
http://dx.doi.org/10.7759/cureus.30414
Descripción
Sumario:Systemic cystic angiomatosis (SCA) is a rare disorder, usually involving the visceral organs with incidental detection during its insidious course. On radiography, it can present as multiple cystic lesions. In rare instances, it can present as mixed lesions (lytic, sclerotic) as was the case with our patient. The disease has a better prognosis than most vascular neoplasms involving the bones. We present a rare case of this disease, involving multiple organs, and presenting with an insidious onset.