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Antioxidant Response in Human X-Linked Adrenoleukodystrophy Fibroblasts

Redox imbalance, mitochondrial dysfunction, and inflammation play a major role in the pathophysiology of X-linked adrenoleukodystrophy (X-ALD), an inherited neurodegenerative disease caused by mutations in the ABCD1 gene, encoding the protein responsible for peroxisomal import and degradation of ver...

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Detalles Bibliográficos
Autores principales:	Petrillo, Sara, D’Amico, Jessica, Nicita, Francesco, Torda, Caterina, Vasco, Gessica, Bertini, Enrico S., Cappa, Marco, Piemonte, Fiorella
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9686530/ https://www.ncbi.nlm.nih.gov/pubmed/36358497 http://dx.doi.org/10.3390/antiox11112125

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