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A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disorder with an absence of pain perception, anhidrosis, heat intolerance, and varying degrees of mental retardation. Though cases of CIPA have innate analgesia, they have been known to have tactile hyperesthesia, thus making anesthes...

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Detalles Bibliográficos
Autores principales: Paul, Maria, Bamba, Charu, Chugh, Vanya, Ravikumar, Nisha, S, Jayaram
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9701320/
https://www.ncbi.nlm.nih.gov/pubmed/36447712
http://dx.doi.org/10.7759/cureus.30790
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author Paul, Maria
Bamba, Charu
Chugh, Vanya
Ravikumar, Nisha
S, Jayaram
author_facet Paul, Maria
Bamba, Charu
Chugh, Vanya
Ravikumar, Nisha
S, Jayaram
author_sort Paul, Maria
collection PubMed
description Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disorder with an absence of pain perception, anhidrosis, heat intolerance, and varying degrees of mental retardation. Though cases of CIPA have innate analgesia, they have been known to have tactile hyperesthesia, thus making anesthesia necessary in case of any surgery. Perioperative complications due to abnormal autonomic functions like bradycardia, hypotension, and hyperthermia are major challenges in the anesthetic management of these cases. Here, we report a case on the anesthetic management of CIPA.
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spelling pubmed-97013202022-11-28 A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis Paul, Maria Bamba, Charu Chugh, Vanya Ravikumar, Nisha S, Jayaram Cureus Anesthesiology Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disorder with an absence of pain perception, anhidrosis, heat intolerance, and varying degrees of mental retardation. Though cases of CIPA have innate analgesia, they have been known to have tactile hyperesthesia, thus making anesthesia necessary in case of any surgery. Perioperative complications due to abnormal autonomic functions like bradycardia, hypotension, and hyperthermia are major challenges in the anesthetic management of these cases. Here, we report a case on the anesthetic management of CIPA. Cureus 2022-10-28 /pmc/articles/PMC9701320/ /pubmed/36447712 http://dx.doi.org/10.7759/cureus.30790 Text en Copyright © 2022, Paul et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Anesthesiology
Paul, Maria
Bamba, Charu
Chugh, Vanya
Ravikumar, Nisha
S, Jayaram
A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis
title A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis
title_full A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis
title_fullStr A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis
title_full_unstemmed A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis
title_short A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis
title_sort boy who knows no pain: anaesthetic management of congenital insensitivity to pain with anhidrosis
topic Anesthesiology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9701320/
https://www.ncbi.nlm.nih.gov/pubmed/36447712
http://dx.doi.org/10.7759/cureus.30790
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