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Acquired von Willebrand syndrome (AVWS) type 2, characterized by decreased high molecular weight multimers, is common in children with severe pulmonary hypertension (PH)

BACKGROUND AND OBJECTIVES: Emerging evidence suggests that increased degradation of von Willebrand factor and decrease in high molecular weight multimers occurs in patients with pulmonary hypertension (PH). However, the link between acquired von Willebrand Syndrome (AVWS) type 2 and PH remains poorl...

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Detalles Bibliográficos
Autores principales:	Wieland, Ivonne, Diekmann, Franziska, Carlens, Julia, Hinze, Laura, Lambeck, Katharina, Jack, Thomas, Hansmann, Georg
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2022
Materias:	Pediatrics
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9701817/ https://www.ncbi.nlm.nih.gov/pubmed/36452355 http://dx.doi.org/10.3389/fped.2022.1012738

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