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A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child

INTRODUCTION: While only a few cases have been reported in pediatrics, subaortic stenosis (SAS) is a gradually progressive disorder rarely seen at birth and infancy, however, it is the most common type of aortic stenosis. It obstructs the blood flow across the left ventricular outflow tract (LVOT)....

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Autores principales: Alamoudi, Loujen O., Alboloshi, Ethar A., Alhnaidi, Malek, Waggass, Rahaf, Alsharif, Salwan, Gazzaz, Abrar M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9712554/
https://www.ncbi.nlm.nih.gov/pubmed/36459852
http://dx.doi.org/10.1016/j.ijscr.2022.107782
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author Alamoudi, Loujen O.
Alboloshi, Ethar A.
Alhnaidi, Malek
Waggass, Rahaf
Alsharif, Salwan
Gazzaz, Abrar M.
author_facet Alamoudi, Loujen O.
Alboloshi, Ethar A.
Alhnaidi, Malek
Waggass, Rahaf
Alsharif, Salwan
Gazzaz, Abrar M.
author_sort Alamoudi, Loujen O.
collection PubMed
description INTRODUCTION: While only a few cases have been reported in pediatrics, subaortic stenosis (SAS) is a gradually progressive disorder rarely seen at birth and infancy, however, it is the most common type of aortic stenosis. It obstructs the blood flow across the left ventricular outflow tract (LVOT). Although the cause is still not well known, different etiologies have been suggested by the literature. While surgical resection is the definitive treatment, recurrence is observed in many patients, nonetheless, LVOT gradient usually progresses over years of follow-up. CASE PRESENTATION: We report the clinical and diagnostic course of a 41-months-old Saudi boy, asymptomatic child who was found to have progressive recurrent subaortic stenosis within a few months which required two redo sternotomy for sub-aortic membrane resection throughout a period of two years. DISCUSSION: SAS is usually detected incidentally in asymptomatic patients requiring an echocardiogram to assess other accompanying congenital heart defects (CHD), or rather potentially arising after repair of CHD. Patient close monitoring is important aspect given the nature of disease progression, re-operation for recurrence demonstrate significant increase over years, re-resection rate was 0 % after one year, 6 % after five years, and 8 % after 10 years. CONCLUSION: Recurrence of LVOT obstruction following sub-aortic membrane resection is common. Long-term follow-up care in postoperative patients is crucial. Majority of patients will need re-operation for recurrence at certain point during course of the disease.
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spelling pubmed-97125542022-12-02 A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child Alamoudi, Loujen O. Alboloshi, Ethar A. Alhnaidi, Malek Waggass, Rahaf Alsharif, Salwan Gazzaz, Abrar M. Int J Surg Case Rep Case Report INTRODUCTION: While only a few cases have been reported in pediatrics, subaortic stenosis (SAS) is a gradually progressive disorder rarely seen at birth and infancy, however, it is the most common type of aortic stenosis. It obstructs the blood flow across the left ventricular outflow tract (LVOT). Although the cause is still not well known, different etiologies have been suggested by the literature. While surgical resection is the definitive treatment, recurrence is observed in many patients, nonetheless, LVOT gradient usually progresses over years of follow-up. CASE PRESENTATION: We report the clinical and diagnostic course of a 41-months-old Saudi boy, asymptomatic child who was found to have progressive recurrent subaortic stenosis within a few months which required two redo sternotomy for sub-aortic membrane resection throughout a period of two years. DISCUSSION: SAS is usually detected incidentally in asymptomatic patients requiring an echocardiogram to assess other accompanying congenital heart defects (CHD), or rather potentially arising after repair of CHD. Patient close monitoring is important aspect given the nature of disease progression, re-operation for recurrence demonstrate significant increase over years, re-resection rate was 0 % after one year, 6 % after five years, and 8 % after 10 years. CONCLUSION: Recurrence of LVOT obstruction following sub-aortic membrane resection is common. Long-term follow-up care in postoperative patients is crucial. Majority of patients will need re-operation for recurrence at certain point during course of the disease. Elsevier 2022-11-21 /pmc/articles/PMC9712554/ /pubmed/36459852 http://dx.doi.org/10.1016/j.ijscr.2022.107782 Text en © 2022 The Authors https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Alamoudi, Loujen O.
Alboloshi, Ethar A.
Alhnaidi, Malek
Waggass, Rahaf
Alsharif, Salwan
Gazzaz, Abrar M.
A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child
title A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child
title_full A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child
title_fullStr A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child
title_full_unstemmed A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child
title_short A Case Report of Recurrent Subaortic Membrane in a 3-Year-Old Saudi Child
title_sort case report of recurrent subaortic membrane in a 3-year-old saudi child
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9712554/
https://www.ncbi.nlm.nih.gov/pubmed/36459852
http://dx.doi.org/10.1016/j.ijscr.2022.107782
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