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Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis w...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Associação Paulista de Medicina - APM
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9721227/ https://www.ncbi.nlm.nih.gov/pubmed/29340502 http://dx.doi.org/10.1590/1516-3180.2017.0120050717 |
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author | Cihan, Yasemin Benderli Kut, Engin Koç, Ali |
author_facet | Cihan, Yasemin Benderli Kut, Engin Koç, Ali |
author_sort | Cihan, Yasemin Benderli |
collection | PubMed |
description | CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa. |
format | Online Article Text |
id | pubmed-9721227 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Associação Paulista de Medicina - APM |
record_format | MEDLINE/PubMed |
spelling | pubmed-97212272022-12-06 Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report Cihan, Yasemin Benderli Kut, Engin Koç, Ali Sao Paulo Med J Case Report CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa. Associação Paulista de Medicina - APM 2018-01-15 /pmc/articles/PMC9721227/ /pubmed/29340502 http://dx.doi.org/10.1590/1516-3180.2017.0120050717 Text en © 2022 by Associação Paulista de Medicina https://creativecommons.org/licenses/by/4.0/This is an open access article distributed under the terms of the Creative Commons license. |
spellingShingle | Case Report Cihan, Yasemin Benderli Kut, Engin Koç, Ali Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
title | Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
title_full | Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
title_fullStr | Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
title_full_unstemmed | Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
title_short | Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
title_sort | recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9721227/ https://www.ncbi.nlm.nih.gov/pubmed/29340502 http://dx.doi.org/10.1590/1516-3180.2017.0120050717 |
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