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Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report

CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis w...

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Autores principales: Cihan, Yasemin Benderli, Kut, Engin, Koç, Ali
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Associação Paulista de Medicina - APM 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9721227/
https://www.ncbi.nlm.nih.gov/pubmed/29340502
http://dx.doi.org/10.1590/1516-3180.2017.0120050717
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author Cihan, Yasemin Benderli
Kut, Engin
Koç, Ali
author_facet Cihan, Yasemin Benderli
Kut, Engin
Koç, Ali
author_sort Cihan, Yasemin Benderli
collection PubMed
description CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa.
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spelling pubmed-97212272022-12-06 Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report Cihan, Yasemin Benderli Kut, Engin Koç, Ali Sao Paulo Med J Case Report CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa. Associação Paulista de Medicina - APM 2018-01-15 /pmc/articles/PMC9721227/ /pubmed/29340502 http://dx.doi.org/10.1590/1516-3180.2017.0120050717 Text en © 2022 by Associação Paulista de Medicina https://creativecommons.org/licenses/by/4.0/This is an open access article distributed under the terms of the Creative Commons license.
spellingShingle Case Report
Cihan, Yasemin Benderli
Kut, Engin
Koç, Ali
Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_full Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_fullStr Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_full_unstemmed Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_short Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_sort recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9721227/
https://www.ncbi.nlm.nih.gov/pubmed/29340502
http://dx.doi.org/10.1590/1516-3180.2017.0120050717
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