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Complications of the Low Phenylalanine Diet for Patients with Phenylketonuria and the Benefits of Increased Natural Protein

Phenylketonuria (PKU) is an inherited disorder in which phenylalanine (Phe) is not correctly metabolized leading to an abnormally high plasma Phe concentration that causes profound neurologic damage if left untreated. The mainstay of treatment for PKU has centered around limiting natural protein in...

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Detalles Bibliográficos
Autores principales:	McWhorter, Nicole, Ndugga-Kabuye, Mesaki K., Puurunen, Marja, Ernst, Sharon L.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9740314/ https://www.ncbi.nlm.nih.gov/pubmed/36500989 http://dx.doi.org/10.3390/nu14234960

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