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Lipidomic Profile Analysis of Lung Tissues Revealed Lipointoxication in Pulmonary Veno-Occlusive Disease

Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary arterial hypertension (PAH) occurring in a heritable form (hPVOD) due to biallelic inactivating mutations of EIF2AK4 (encoding GCN2, general control nonderepressible 2) or in a sporadic form in older age (sPVOD), following exposure...

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Detalles Bibliográficos
Autores principales: Khoury, Spiro, Beauvais, Antoine, Colas, Jenny, Saint-Martin Willer, Anaïs, Perros, Frédéric, Humbert, Marc, Vandebrouck, Clarisse, Montani, David, Ferreira, Thierry, Antigny, Fabrice
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9775349/
https://www.ncbi.nlm.nih.gov/pubmed/36551306
http://dx.doi.org/10.3390/biom12121878

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