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Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration
Dermatofibrosarcoma protuberans (DFSP) is a rare, locally aggressive spindle cell mesenchymal tumor arising in the dermis, with low metastatic potential. The most commonly affected sites are the trunk and proximal extremities; rarely are acral sites involved. Atrophic DFSP is a rare form of DFSP, th...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9776950/ https://www.ncbi.nlm.nih.gov/pubmed/36547218 http://dx.doi.org/10.3390/dermatopathology9040044 |
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author | Mahboob, Anber Turgeon, Claire Qasim, Syeda Usmani, Arif |
author_facet | Mahboob, Anber Turgeon, Claire Qasim, Syeda Usmani, Arif |
author_sort | Mahboob, Anber |
collection | PubMed |
description | Dermatofibrosarcoma protuberans (DFSP) is a rare, locally aggressive spindle cell mesenchymal tumor arising in the dermis, with low metastatic potential. The most commonly affected sites are the trunk and proximal extremities; rarely are acral sites involved. Atrophic DFSP is a rare form of DFSP, that is morphologically different but histologically similar to DFSP. It commonly affects young adults between the ages of 20 to 50 years. The current management strategy for atrophic DFSP is surgical excision with long-term follow-up to detect any recurrence. Only one known case of atrophic DFSP with eosinophilic infiltration is what makes our case an exceptionally rare presentation. |
format | Online Article Text |
id | pubmed-9776950 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-97769502022-12-23 Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration Mahboob, Anber Turgeon, Claire Qasim, Syeda Usmani, Arif Dermatopathology (Basel) Case Report Dermatofibrosarcoma protuberans (DFSP) is a rare, locally aggressive spindle cell mesenchymal tumor arising in the dermis, with low metastatic potential. The most commonly affected sites are the trunk and proximal extremities; rarely are acral sites involved. Atrophic DFSP is a rare form of DFSP, that is morphologically different but histologically similar to DFSP. It commonly affects young adults between the ages of 20 to 50 years. The current management strategy for atrophic DFSP is surgical excision with long-term follow-up to detect any recurrence. Only one known case of atrophic DFSP with eosinophilic infiltration is what makes our case an exceptionally rare presentation. MDPI 2022-11-27 /pmc/articles/PMC9776950/ /pubmed/36547218 http://dx.doi.org/10.3390/dermatopathology9040044 Text en © 2022 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Case Report Mahboob, Anber Turgeon, Claire Qasim, Syeda Usmani, Arif Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration |
title | Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration |
title_full | Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration |
title_fullStr | Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration |
title_full_unstemmed | Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration |
title_short | Atrophic Dermatofibrosarcoma Protuberans with Eosinophilic Infiltration |
title_sort | atrophic dermatofibrosarcoma protuberans with eosinophilic infiltration |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9776950/ https://www.ncbi.nlm.nih.gov/pubmed/36547218 http://dx.doi.org/10.3390/dermatopathology9040044 |
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