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Desmoid fibromatosis infiltrating left adrenal gland and kidney
Desmoid fibromatosis is a rare, benign, locally aggressive fibroblastic proliferation that may occur in almost any anatomical location. Due to its rarity and unpredictable clinical course, there has not been a standard guideline of treatment. We encountered a case of desmoid fibromatosis in our cent...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9792179/ https://www.ncbi.nlm.nih.gov/pubmed/36578629 http://dx.doi.org/10.1093/jscr/rjac585 |
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author | Tee, Sui Wu Richards, Avisha Tan, Yi Han Jeyabalan, Dhinisya Durairaj, Gunaseelan |
author_facet | Tee, Sui Wu Richards, Avisha Tan, Yi Han Jeyabalan, Dhinisya Durairaj, Gunaseelan |
author_sort | Tee, Sui Wu |
collection | PubMed |
description | Desmoid fibromatosis is a rare, benign, locally aggressive fibroblastic proliferation that may occur in almost any anatomical location. Due to its rarity and unpredictable clinical course, there has not been a standard guideline of treatment. We encountered a case of desmoid fibromatosis in our centre. A young lady previously fit and well was referred for a symptomatic, rapidly growing left sided abdominal mass. Otherwise, she denied any bowel related symptoms or constitutional manifestation. Imaging demonstrated a large well-defined lobulated solid-cystic mass extending from vertebral level T10 to L5, measuring 10.5 cm × 15 cm × 23 cm. The mass was in close proximity with the left adrenal gland, left kidney, pancreas and spleen. Ultrasound guided biopsy interpreted it as a fibroblastic or myelofibroblastic tumour, favouring desmoid fibromatosis. Surgery was then performed where the mass was removed along with the left adrenal gland and kidney. Post-operative care was complicated with pulmonary embolism, hospital-acquired pneumonia and pancreatitis. |
format | Online Article Text |
id | pubmed-9792179 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-97921792022-12-27 Desmoid fibromatosis infiltrating left adrenal gland and kidney Tee, Sui Wu Richards, Avisha Tan, Yi Han Jeyabalan, Dhinisya Durairaj, Gunaseelan J Surg Case Rep Case Report Desmoid fibromatosis is a rare, benign, locally aggressive fibroblastic proliferation that may occur in almost any anatomical location. Due to its rarity and unpredictable clinical course, there has not been a standard guideline of treatment. We encountered a case of desmoid fibromatosis in our centre. A young lady previously fit and well was referred for a symptomatic, rapidly growing left sided abdominal mass. Otherwise, she denied any bowel related symptoms or constitutional manifestation. Imaging demonstrated a large well-defined lobulated solid-cystic mass extending from vertebral level T10 to L5, measuring 10.5 cm × 15 cm × 23 cm. The mass was in close proximity with the left adrenal gland, left kidney, pancreas and spleen. Ultrasound guided biopsy interpreted it as a fibroblastic or myelofibroblastic tumour, favouring desmoid fibromatosis. Surgery was then performed where the mass was removed along with the left adrenal gland and kidney. Post-operative care was complicated with pulmonary embolism, hospital-acquired pneumonia and pancreatitis. Oxford University Press 2022-12-25 /pmc/articles/PMC9792179/ /pubmed/36578629 http://dx.doi.org/10.1093/jscr/rjac585 Text en Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2022. https://creativecommons.org/licenses/by/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted reuse, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Tee, Sui Wu Richards, Avisha Tan, Yi Han Jeyabalan, Dhinisya Durairaj, Gunaseelan Desmoid fibromatosis infiltrating left adrenal gland and kidney |
title | Desmoid fibromatosis infiltrating left adrenal gland and kidney |
title_full | Desmoid fibromatosis infiltrating left adrenal gland and kidney |
title_fullStr | Desmoid fibromatosis infiltrating left adrenal gland and kidney |
title_full_unstemmed | Desmoid fibromatosis infiltrating left adrenal gland and kidney |
title_short | Desmoid fibromatosis infiltrating left adrenal gland and kidney |
title_sort | desmoid fibromatosis infiltrating left adrenal gland and kidney |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9792179/ https://www.ncbi.nlm.nih.gov/pubmed/36578629 http://dx.doi.org/10.1093/jscr/rjac585 |
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