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Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report
INTRODUCTION: and importance: Ebstein's anomaly (EA) is a rare congenital heart disease characterized by apical displacement of the tricuspid valve associated with atrialization of the right ventricle. Most of the cases are diagnosed in childhood but asymptomatic cases may remain undiagnosed an...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9793134/ https://www.ncbi.nlm.nih.gov/pubmed/36582865 http://dx.doi.org/10.1016/j.amsu.2022.104821 |
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author | Poudel, Priyanka Pathak, Sujan Bhattarai, Nishan |
author_facet | Poudel, Priyanka Pathak, Sujan Bhattarai, Nishan |
author_sort | Poudel, Priyanka |
collection | PubMed |
description | INTRODUCTION: and importance: Ebstein's anomaly (EA) is a rare congenital heart disease characterized by apical displacement of the tricuspid valve associated with atrialization of the right ventricle. Most of the cases are diagnosed in childhood but asymptomatic cases may remain undiagnosed and survive until old age. CASE PRESENTATION: We present a rare case of Ebstein's Anomaly with pericardial effusion which was diagnosed for the first time in her mid-fifties when she developed atrial fibrillation and right heart failure with severe tricuspid regurgitation, which was managed medically. CLINICAL DISCUSSION: The patient with Ebstein's anomaly can be found even at an older age with variable presentation and the association with pericardial effusion although very rare can present in such patients. CONCLUSION: Ebstein's anomaly despite being a rare congenital condition can present clinically even beyond the age of fifty without any previous diagnosis and surgical intervention for the condition. It usually presents with features of heart failure and arrhythmia but can also have a rare association like pericardial effusion. |
format | Online Article Text |
id | pubmed-9793134 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-97931342022-12-28 Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report Poudel, Priyanka Pathak, Sujan Bhattarai, Nishan Ann Med Surg (Lond) Case Report INTRODUCTION: and importance: Ebstein's anomaly (EA) is a rare congenital heart disease characterized by apical displacement of the tricuspid valve associated with atrialization of the right ventricle. Most of the cases are diagnosed in childhood but asymptomatic cases may remain undiagnosed and survive until old age. CASE PRESENTATION: We present a rare case of Ebstein's Anomaly with pericardial effusion which was diagnosed for the first time in her mid-fifties when she developed atrial fibrillation and right heart failure with severe tricuspid regurgitation, which was managed medically. CLINICAL DISCUSSION: The patient with Ebstein's anomaly can be found even at an older age with variable presentation and the association with pericardial effusion although very rare can present in such patients. CONCLUSION: Ebstein's anomaly despite being a rare congenital condition can present clinically even beyond the age of fifty without any previous diagnosis and surgical intervention for the condition. It usually presents with features of heart failure and arrhythmia but can also have a rare association like pericardial effusion. Elsevier 2022-11-05 /pmc/articles/PMC9793134/ /pubmed/36582865 http://dx.doi.org/10.1016/j.amsu.2022.104821 Text en © 2022 The Authors https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Poudel, Priyanka Pathak, Sujan Bhattarai, Nishan Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report |
title | Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report |
title_full | Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report |
title_fullStr | Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report |
title_full_unstemmed | Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report |
title_short | Ebstein's anomaly with pericardial effusion in a 55-year-old lady: A case report |
title_sort | ebstein's anomaly with pericardial effusion in a 55-year-old lady: a case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9793134/ https://www.ncbi.nlm.nih.gov/pubmed/36582865 http://dx.doi.org/10.1016/j.amsu.2022.104821 |
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