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Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman

Cor triatriatum sinister is a rare congenital heart disease characterized by an additional fibromuscular membrane in the left atrium. Cardioembolic stroke is a rare complication of cor triatriatum sinister, especially among women. We hereby describe the case of an 18-year-old female patient, without...

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Autores principales: Szabo, Timea Magdolna, Heidenhoffer, Erhard, Kirchmaier, Ádám, Pelok, Benedek, Frigy, Attila
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9818967/
https://www.ncbi.nlm.nih.gov/pubmed/36611389
http://dx.doi.org/10.3390/diagnostics13010097
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author Szabo, Timea Magdolna
Heidenhoffer, Erhard
Kirchmaier, Ádám
Pelok, Benedek
Frigy, Attila
author_facet Szabo, Timea Magdolna
Heidenhoffer, Erhard
Kirchmaier, Ádám
Pelok, Benedek
Frigy, Attila
author_sort Szabo, Timea Magdolna
collection PubMed
description Cor triatriatum sinister is a rare congenital heart disease characterized by an additional fibromuscular membrane in the left atrium. Cardioembolic stroke is a rare complication of cor triatriatum sinister, especially among women. We hereby describe the case of an 18-year-old female patient, without a past medical history, presenting with cardioembolic stroke in the territory of the right posterior cerebral artery. During extensive diagnostic work-up, nonrestrictive cor triatriatum sinister and patent foramen ovale were diagnosed using transthoracic and transesophageal echocardiography. In clinical practice, it is important to identify congenital cardiac defects as potential substrates for cardioembolism in young patients. In our case, cor triatriatum sinister presenting as ischemic stroke was diagnosed, which is an uncommon finding, especially in young females. Determining the optimal management strategy for patients with cor triatriatum sinister complicated by cardioembolic stroke requires a multidisciplinary approach.
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spelling pubmed-98189672023-01-07 Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman Szabo, Timea Magdolna Heidenhoffer, Erhard Kirchmaier, Ádám Pelok, Benedek Frigy, Attila Diagnostics (Basel) Interesting Images Cor triatriatum sinister is a rare congenital heart disease characterized by an additional fibromuscular membrane in the left atrium. Cardioembolic stroke is a rare complication of cor triatriatum sinister, especially among women. We hereby describe the case of an 18-year-old female patient, without a past medical history, presenting with cardioembolic stroke in the territory of the right posterior cerebral artery. During extensive diagnostic work-up, nonrestrictive cor triatriatum sinister and patent foramen ovale were diagnosed using transthoracic and transesophageal echocardiography. In clinical practice, it is important to identify congenital cardiac defects as potential substrates for cardioembolism in young patients. In our case, cor triatriatum sinister presenting as ischemic stroke was diagnosed, which is an uncommon finding, especially in young females. Determining the optimal management strategy for patients with cor triatriatum sinister complicated by cardioembolic stroke requires a multidisciplinary approach. MDPI 2022-12-29 /pmc/articles/PMC9818967/ /pubmed/36611389 http://dx.doi.org/10.3390/diagnostics13010097 Text en © 2022 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/).
spellingShingle Interesting Images
Szabo, Timea Magdolna
Heidenhoffer, Erhard
Kirchmaier, Ádám
Pelok, Benedek
Frigy, Attila
Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman
title Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman
title_full Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman
title_fullStr Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman
title_full_unstemmed Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman
title_short Cor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman
title_sort cor triatriatum sinister presenting as cardioembolic stroke in a young woman
topic Interesting Images
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9818967/
https://www.ncbi.nlm.nih.gov/pubmed/36611389
http://dx.doi.org/10.3390/diagnostics13010097
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