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Quantitative magnetic resonance imaging assessment of muscle composition in myotonic dystrophy mice

Myotonic dystrophy type 1 (DM1) is a severe autosomal dominant neuromuscular disease in which the musculoskeletal system contributes substantially to overall mortality and morbidity. DM1 stems from a noncoding CTG trinucleotide repeat expansion in the DMPK gene. The human skeletal actin long repeat...

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Detalles Bibliográficos
Autores principales:	Bargiela, Ariadna, Ten-Esteve, Amadeo, Martí-Bonmatí, Luis, Sevilla, Teresa, Perez Alonso, Manuel, Artero, Ruben
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Nature Publishing Group UK 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9831979/ https://www.ncbi.nlm.nih.gov/pubmed/36627397 http://dx.doi.org/10.1038/s41598-023-27661-w

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