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Cystic fibrosis rabbits develop spontaneous hepatobiliary lesions and CF-associated liver disease (CFLD)-like phenotypes
Cystic fibrosis (CF) is an autosomal recessive genetic disease affecting multiple organs. Approximately 30% CF patients develop CF-related liver disease (CFLD), which is the third most common cause of morbidity and mortality of CF. CFLD is progressive, and many of the severe forms eventually need li...
Autores principales: | Wu, Qingtian, Liang, Xiubin, Hou, Xia, Song, Zhenfeng, Bouhamdan, Mohamad, Qiu, Yining, Koike, Yui, Rajagopalan, Carthic, Wei, Hong-Guang, Jiang, Hong, Hish, Gerry, Zhang, Jifeng, Chen, Y Eugene, Jin, Jian-Ping, Xu, Jie, Zhang, Kezhong, Sun, Fei |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9832953/ https://www.ncbi.nlm.nih.gov/pubmed/36712930 http://dx.doi.org/10.1093/pnasnexus/pgac306 |
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