Cargando…

Diagnostic agreement among experts assessing adults presenting with possible cystic fibrosis: need for improvement and implications for patient care

BACKGROUND: Increasing awareness of milder presentations of cystic fibrosis (CF) and greater interest in non-CF bronchiectasis are likely to lead to more CF screening by respiratory clinicians. As a result, adults who may not strictly fulfil CF diagnostic criteria yet display evidence of abnormal CF...

Descripción completa

Detalles Bibliográficos
Autores principales:	Franciosi, Alessandro N., Tanzler, April, Goodwin, Jodi, Wilcox, Pearce G., Solomon, George M., Faro, Albert, McElvaney, Noel G., Downey, Damian G., Quon, Bradley S.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	European Respiratory Society 2022
Materias:	Original Research Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9835972/ https://www.ncbi.nlm.nih.gov/pubmed/36655218 http://dx.doi.org/10.1183/23120541.00227-2022

Ejemplares similares

Experience to date with CFTR modulators during pregnancy and breastfeeding in the British Columbia Cystic Fibrosis clinic
por: Goodwin, Jodi, et al.
Publicado: (2022)

Sex disparities in cystic fibrosis: review on the effect of female sex hormones on lung pathophysiology and outcomes
por: Lam, Grace Y., et al.
Publicado: (2021)

Cystic Fibrosis Respiratory Microbiology Monitoring during a Global Pandemic: Lessons Learned from a Shift to Telehealth
por: Franciosi, Alessandro N., et al.
Publicado: (2022)

Hypertonic Saline in Treatment of Pulmonary Disease in Cystic Fibrosis
por: Reeves, Emer P., et al.
Publicado: (2012)

Targeting IgG Autoantibodies for Improved Cytotoxicity of Bactericidal Permeability Increasing Protein in Cystic Fibrosis
por: McQuillan, Karen, et al.
Publicado: (2020)

Alpha-1 antitrypsin for cystic fibrosis complicated by severe cytokinemic COVID-19
por: McElvaney, Oliver J, et al.
Publicado: (2021)

Evaluating Adult Cystic Fibrosis Care in BC: Disparities in Access to a Multidisciplinary Treatment Centre
por: Roberts, James M., et al.
Publicado: (2016)

The Involvement of Glycosaminoglycans in Airway Disease Associated with Cystic Fibrosis
por: Reeves, Emer P., et al.
Publicado: (2011)

Patient knowledge and pulmonary medication adherence in adult patients with cystic fibrosis
por: Lin, Ann Hsu-An, et al.
Publicado: (2017)

TeleHealth or TeleWealth? Equity challenges for the future of cystic fibrosis care (Commentary)()
por: Franciosi, Alessandro N, et al.
Publicado: (2021)

Diagnosing α(1)-antitrypsin deficiency: how to improve the current algorithm
por: McElvaney, Noel G.
Publicado: (2015)

The Extrapulmonary Effects of Cystic Fibrosis Transmembrane Conductance Regulator Modulators in Cystic Fibrosis
por: Sergeev, Valentine, et al.
Publicado: (2020)

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences
por: Lavelle, Gillian M., et al.
Publicado: (2016)

Editorial: Novel Anti-Inflammatory Approaches for Cystic Fibrosis Lung Disease: Identification of Molecular Targets and Design of Innovative Therapies
por: Ribeiro, Carla Maria Pedrosa, et al.
Publicado: (2021)

Airway inflammatory markers in individuals with cystic fibrosis and non-cystic fibrosis bronchiectasis
por: Bergin, David A, et al.
Publicado: (2013)

miRNA-221 is elevated in cystic fibrosis airway epithelial cells and regulates expression of ATF6
por: Oglesby, Irene K, et al.
Publicado: (2015)

Interleukin-6: obstacles to targeting a complex cytokine in critical illness
por: McElvaney, Oliver J, et al.
Publicado: (2021)

Plasma sCD14 as a Biomarker to Predict Pulmonary Exacerbations in Cystic Fibrosis
por: Quon, Bradley S., et al.
Publicado: (2014)

Nebulized levofloxacin for chronic Burkholderia cenocepacia pulmonary infection in cystic fibrosis: A case report
por: Dagenais, Renée VE., et al.
Publicado: (2022)

The importance of CFTR expression for neutrophil function in patients with Cystic Fibrosis
por: Jundi, B, et al.
Publicado: (2015)

Reply to Blot et al. and to Inoue et al.
por: McElvaney, Oliver J., et al.
Publicado: (2021)

Altered Degranulation and pH of Neutrophil Phagosomes Impacts Antimicrobial Efficiency in Cystic Fibrosis
por: Hayes, Elaine, et al.
Publicado: (2020)

Impaired Airway Epithelial Barrier Integrity in Response to Stenotrophomonas maltophilia Proteases, Novel Insights Using Cystic Fibrosis Bronchial Epithelial Cell Secretomics
por: Molloy, Kevin, et al.
Publicado: (2020)

Optic Disc Swelling and Vision Loss in a Patient with Cystic Fibrosis and Diabetes
por: Iosfina, Ioulia, et al.
Publicado: (2013)

Worsening pulmonary outcomes during sex reassignment therapy in a transgender female with cystic fibrosis (CF) and asthma/allergic bronchopulmonary aspergillosis: a case report
por: Lam, G. Y., et al.
Publicado: (2020)

Inhibition of Toll-Like Receptor 2-Mediated Interleukin-8 Production in Cystic Fibrosis Airway Epithelial Cells via the α7-Nicotinic Acetylcholine Receptor
por: Greene, Catherine M., et al.
Publicado: (2010)

Global burden of nontuberculous mycobacteria in the cystic fibrosis population: a systematic review and meta-analysis
por: Prieto, Miguel D., et al.
Publicado: (2023)

Neutrophil Membrane Cholesterol Content is a Key Factor in Cystic Fibrosis Lung Disease
por: White, Michelle M., et al.
Publicado: (2017)

Is There a Therapeutic Role for Selenium in Alpha-1 Antitrypsin Deficiency?
por: Greene, Catherine M., et al.
Publicado: (2013)

Short-term effects of Lumacaftor/Ivacaftor (Orkambi™) on exertional symptoms, exercise performance, and ventilatory responses in adults with cystic fibrosis
por: Quon, Bradley S., et al.
Publicado: (2020)

Clinical utility of C-reactive protein to predict treatment response during cystic fibrosis pulmonary exacerbations
por: Sharma, Ashutosh, et al.
Publicado: (2017)

An investigation of IL-8 degradation in response to PA401 compared to hypertonic saline in bronchoalveolar lavage fluid of Cystic Fibrosis patients
por: Kerr, H, et al.
Publicado: (2015)

Gene targeted therapeutics for liver disease in alpha-1 antitrypsin deficiency
por: McLean, Caitriona, et al.
Publicado: (2009)

MicroRNAs in inflammatory lung disease - master regulators or target practice?
por: Oglesby, Irene K, et al.
Publicado: (2010)

The role of TIM-containing molecules in airway disease and their potential as therapeutic targets
por: Vega-Carrascal, Isabel, et al.
Publicado: (2012)

Alpha-1 antitrypsin regulates neutrophil reactive oxygen species production via inhibition of key players of the respiratory burst oxidase system
por: Alfawaz, Bader, et al.
Publicado: (2013)

miR-224-5p and miR-545-5p Levels Relate to Exacerbations and Lung Function in a Pilot Study of X-Linked MicroRNA Expression in Cystic Fibrosis Monocytes
por: McKiernan, Paul J., et al.
Publicado: (2021)

Intracellular Secretory Leukoprotease Inhibitor Modulates Inositol 1,4,5-Triphosphate Generation and Exerts an Anti-Inflammatory Effect on Neutrophils of Individuals with Cystic Fibrosis and Chronic Obstructive Pulmonary Disease
por: Reeves, Emer P., et al.
Publicado: (2013)

Dysregulated plasma lipid mediator profiles in critically ill COVID-19 patients
por: Palmas, Francesco, et al.
Publicado: (2021)

Exploring the views of healthcare professionals on increasing smoking cessation advice for patients
por: Ho, ShuYing, et al.
Publicado: (2013)

Cannot write session to /tmp/vufind_sessions/sess_21cl0tdlgratgbpvnb0ttb2l47