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Adult‐onset still's disease and budd‐chiari syndrome: A case report

Adult onset still's disease (AOSD) is a rare autoinflammatory disease displaying with a wide range of non‐specific symptoms and budd‐chiari syndrome (BCS) is an uncommon disorder characterized by obstruction of hepatic venous outflow. We present the case of a young patient who presented with pe...

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Autores principales: Hakamifard, Atousa, Aria, Amir, Momenzadeh, Mahnaz
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9842873/
https://www.ncbi.nlm.nih.gov/pubmed/36694654
http://dx.doi.org/10.1002/ccr3.6825
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author Hakamifard, Atousa
Aria, Amir
Momenzadeh, Mahnaz
author_facet Hakamifard, Atousa
Aria, Amir
Momenzadeh, Mahnaz
author_sort Hakamifard, Atousa
collection PubMed
description Adult onset still's disease (AOSD) is a rare autoinflammatory disease displaying with a wide range of non‐specific symptoms and budd‐chiari syndrome (BCS) is an uncommon disorder characterized by obstruction of hepatic venous outflow. We present the case of a young patient who presented with persistent fever, sore throat, elbow, hand fingers and knees arthralgia with abdominal pain. The patient's symptoms had started 7 days before the referral. Imaging and laboratory data led to the diagnosis of BCS in the context of AOSD. The patient treated with corticosteroid in combination of warfarin with favorable outcome and complete improvement of signs and symptoms. We came to this conclusion AOSD complicated with BCS is a rare but potentially life‐threatening entity. Clinicians should be aware of this complication.
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spelling pubmed-98428732023-01-23 Adult‐onset still's disease and budd‐chiari syndrome: A case report Hakamifard, Atousa Aria, Amir Momenzadeh, Mahnaz Clin Case Rep Case Report Adult onset still's disease (AOSD) is a rare autoinflammatory disease displaying with a wide range of non‐specific symptoms and budd‐chiari syndrome (BCS) is an uncommon disorder characterized by obstruction of hepatic venous outflow. We present the case of a young patient who presented with persistent fever, sore throat, elbow, hand fingers and knees arthralgia with abdominal pain. The patient's symptoms had started 7 days before the referral. Imaging and laboratory data led to the diagnosis of BCS in the context of AOSD. The patient treated with corticosteroid in combination of warfarin with favorable outcome and complete improvement of signs and symptoms. We came to this conclusion AOSD complicated with BCS is a rare but potentially life‐threatening entity. Clinicians should be aware of this complication. John Wiley and Sons Inc. 2023-01-16 /pmc/articles/PMC9842873/ /pubmed/36694654 http://dx.doi.org/10.1002/ccr3.6825 Text en © 2023 Isfahan university of medical science. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Report
Hakamifard, Atousa
Aria, Amir
Momenzadeh, Mahnaz
Adult‐onset still's disease and budd‐chiari syndrome: A case report
title Adult‐onset still's disease and budd‐chiari syndrome: A case report
title_full Adult‐onset still's disease and budd‐chiari syndrome: A case report
title_fullStr Adult‐onset still's disease and budd‐chiari syndrome: A case report
title_full_unstemmed Adult‐onset still's disease and budd‐chiari syndrome: A case report
title_short Adult‐onset still's disease and budd‐chiari syndrome: A case report
title_sort adult‐onset still's disease and budd‐chiari syndrome: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9842873/
https://www.ncbi.nlm.nih.gov/pubmed/36694654
http://dx.doi.org/10.1002/ccr3.6825
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